Transcript Document

INTRODUCTION TO
RHEUMATOLOGY
The origins of Rheumatology


Rheumatology - a branch of medicine devoted to the
study of rheumatic diseases and disorders of the
function and / or structure of the musculoskeletal system.
In the I century AD was the first appeared in the
literature, the concept of rheuma (revma). The word
"rheuma" of Greek origin. Rheuma refers to "a
substance that flows", probably formed from phlegm.
This is the "primary juice," by definition of the ancients,
which was formed in the brain and flowed in different
parts of the body, causing illness.
The origins of Rheumatology

In 1642, the term
"rheumatism" was
introduced in the
literature by french
physician Dr. G.
Baillou, who supposed
that arthritis can be a
manifestation of
systemic disease.
The origins of Rheumatology

In 1928, in the USA Dr. R.
Pemberton organized the
American Committee for the
treatment of rheumatism,
which was renamed the
American Association for the
Study and Treatment of
rheumatic diseases (1934),
followed by the American
Association of rheumaticism
(1937) and, finally, the
American Rheumatology
Association (1988).
The origins of Rheumatology


In 1940, Bernard Comroe suggested the
term "rheumatologist.“
In 1949, Hollander uses the term
"rheumatology" in his textbook on
arthritis and painful condition (Arthritis
and Allied Conditions).
History of the discovery of some
rheumatic diseases
Acute rheumatic fever
Acute rheumatic fever



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
The doctrine of rheumatism has a long history. For the first time
information about rheumatic arthritis appeared in the writings
of Hippocrates. There was humoralism (Latin humor - fluid) current through the joint process.
In the early XX century, all were regarded as diseases of the
joints and rheumatism.
Classic works consecrated to the ARF, have been written by
Jean-Bapite Bomllard and Walter B Cheadle and published in
1836, which detailed the "rheumatic arthritis" and carditis.
At one time Lasegue said: "Rheumatism licks the joints but bites
the heart.“
S. Botkin has been shown that ARF affects many organs:
kidneys, skin, nervous system, liver and lungs.
Acute rheumatic fever


In 1904 morphologist Ludwig Aschoff first
discovered and described the morphological
substrate of rheumatic fever - a kind of cell
granuloma. In 1929 Talalayev showed that
rheumatic granuloma Aschoff - only one stage, but
it has 3 phases: exudative, proliferative phase, cell
proliferation and sclerosis. So now the rheumatic
granuloma-called Aschoff Talalayev.
In 1933, Rebecca Lancefield was divided into
groups hemolytic streptococci, helping researchers
clarify the epidemiology of the disease. For the
first time the criteria for leadership in the
diagnosis of ARF were developed by Dr. T Duckett
Jones and published in 1944. Later they were
adopted and revised by the American Heart
Association.
Rheumatoid arthritis
Rheumatoid arthritis
The earliest signs of rheumatoid arthritis
were found in 4500 BC. They were found on
the remains of skeletons of Indians in
Tennessee, USA.
 The first paper describing the symptoms are
very reminiscent of the symptoms of
rheumatoid arthritis dates back to 123 a
year.



The first clinical description of this
pathology in 1800, is credited with
Augustin-Jacob Landre-Beauvais. The
author called the disease variant of
gout - a "simple asthenic gout" (goutte
asthenique primitif).
Benjamin Brodie described the slow
progression of synovitis by involving
joint capsule and tendon sheath.

Joint swelling in early
rheumatoid arthritis
Deformities of long-standing
rheumatoid arthritis
Rheumatoid arthritis

A. Garrod suggested
the term "rheumatoid
arthritis" in 1858 and
differentiate it from
gout in 1892, the
disease got its present
name.
Systemic lupus erythematosus


The name lupus, the Latin
version as Lupus
erythematosus, comes from
the Latin "lupus", which
means wolf and
"eritematozus" - red,
because of its similarity to
the bite injuries hungry wolf.

This disease is known to doctors since 1828,
after describing the French dermatologist
Biett skin symptoms
45 years later
Kaposhi
(dermatologist)
observed that
some patients
with skin
symptoms are
also symptoms
of internal
organs.


In 1845, Ferdinand
von Hebra described
a rash on the type of
"butterflies" on her
nose and cheeks.
Systemic lupus erythematosus
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In 1948,William Hargraves described the LE-cells.
This discovery allowed doctors to identify many
patients with systemic lupus erythematosus.
In 1956, Miescher, described the absorption of LEcell factor kernels.
In 1958, George Friou described a method for
identification of antinuclear antibodies.
Spondyloarthropathies
(ankylosing spondylitis)
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The archaeological study of Egyptian mummies found the
disease, which is now called ankylosing spondylitis is
known to mankind since ancient times.
The first historical description of the disease in the
literature refers to 1559, when Realdo Colombo
described the two skeletons with typical changes of
ankylosing spondylitis in his book "Anatomy.“
100 years later, in 1693, an Irish physician Bernard
Connor described the skeleton of a man with signs of
scoliosis, in which the sacrum, hip bone, lumbar vertebrae
and 10 thoracic vertebrae with ribs are fused into one
bone.
Spondyloarthropathies
(ankylosing spondylitis)
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
In the late 1890s, Russian
doctor, Vladimir Bekhterev
and French doctors Adolf
Strumpell and Pierre Marie
described ankylosing
spondylitis.
Linking disease to a gene
class I HLA-B27 belongs to the
Americans Lee Schlosstein,
Rodney Bluestone and Paul
Terasaki, as well as the British
Derrick Brewerton, Caffrey
and Nichols.
Classification of rheumatic / musculoskeletal
syndromes in different years
Rheumatology as a specialty
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

Rheumatology as an independent scientific and
practical discipline was formed 45 years ago.
Rheumatic diseases are one of the most common
pathologies of the human body.
The term "rheumatic disease" include a variety of
origins of the disease predominantly systemic, less
local character, proceeding with persistent or
transient articular syndrome.
The origins of the classification

Theoretical basis for combining these various
diseases in the same group was the fact that their
basis is a preferential loss of connective tissue, as
dense, which include the dermis, tendons, ligaments,
cartilage, bone and others, and its special types
(synovial and serous membranes, basal membranes
of blood vessels and epithelium, etc.).
Working classification and nomenclature of
rheumatic diseases (1999)
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
I. Rheumatism (rheumatic fever)
II. Diffuse diseases of connective tissue
1.0. Lupus Erythematosus
 2.0. Systemic Scleroderma
 3.0. Diffuse Fasciitis
 4.0. Dermatomyositis (polimiozit)
 5.0. Disease Šhoegren
 6.0. Mixed connective tissue disease
 7.0. Rheumatic polimialgia
 8.0. Recurrent polihondritis, including Tietze disease
 9.0. Recurrent pannikulitis (Weber-Christian disease)

 Working
classification and nomenclature of rheumatic
diseases (1999)
 III. Systemic Vasculitis
1.0. periarteritis nodosa
 2.0. Granulomatous arteritis:

2.1. Wegener's granulomatosis
2.2. Eosinophilic granulomatous vasculitis
2.3. Giant cell arteritis temporal (Horton's disease)
2.4. Nonspecific aortoarteriit (Takayasu's disease)
3.0. Hyperergic angiitis
3.1. Hemorrhagic vasculitis (Henoch disease - purpura)
3.2. Goodpasture's syndrome
3.3. Mixed cryoglobulinemia (cryoglobulinemc purpura)
4.0. Thromboangiitis obliterans (Buerger's disease)
5.0. Behcet's syndrome
6.0. Kawasaki syndrome (muco-cutaneous-glandular syndrome)
Working classification and nomenclature of
rheumatic diseases (1999)

IV. Rheumatoid arthritis
V. Juvenile arthritis
VI. Ankylosing spondylitis (Bechterew)
VII. Arthritis, combined with spondylarthritis
1.0. psoriatic arthritis
2.0. Reiter's disease
3.0. Arthritis in chronic nonspecific bowel disease
(ulcerative colitis, ileitis regionar-ny Crohn's disease)
4.0. Arthritis, and (or) sacroiliitis unspecified
etiology

VIII. Arthritis associated with infection
1.0. infectious arthritis
1.1. Bacterial (staphylococcal, brucellosis, syphilis,
spirochetal, mycobacterial, tuberculosis, etc.)
1.1.1. Lyme disease
1.1.2. Whipple's disease
1.2. viral
1.3. fungal
1.4. parasitic

2.0. Reactive arthritis
2.1. Postenterocolitic (shigellosis, yersiniosis,
salmonellosis, klebsiellosis, etc.)
2.2. Urogenital (excluding Reiter's disease and
gonorrhea)
2.3. After nasopharyngeal infection
2.4. After vaccination

2.0. Реактивные артриты

2.1. Постэнтероколитические (шигеллез, иерсиниоз, сальмонеллез,
клебсиеллез и др.)

2.2. Урогенитальные (исключая болезнь Рейтера и гонорею)

2.3. После носоглоточной инфекции

2.4. Поствакцинальные

IX. microcrystalline arthritis
1.0. primary gout
2.0. Gout secondary (drug, renal insufficiency,
lead intoxication, etc.)
3.0. Chondrocalcinosis (pseudogout)
4.0. hydroxyapatite arthropathy
Рабочая классификация и номенклатура
ревматических болезней (1999)

IX. Микрокристаллические артриты
 1.0.
Подагра первичная
 2.0. Подагра вторичная (лекарственная, при
почечной недостаточности, свинцовой
интоксикации и др.)
 3.0. Хондрокальциноз (псевдоподагра)
 4.0. Гидроксиапатитовая артропатия

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X. osteoarthritis
XI. Other joint diseases
1.0. palindromic rheumatism
2.0. intermittent hydrarthrosis
3.0. multiple retikulohystiocytosis
4.0. Sinovioma
5.0. chondromatosis of the joint
6.0. Villonodulary synovitis


X. Остеоартроз
XI. Другие болезни суставов
 1.0.
Палиндромный ревматизм
 2.0. Интермиттирующий гидрартроз
 3.0. Множественный ретикулогистиоцитоз
 4.0. Синовиома
 5.0. Хондроматоз сустава
 6.0. Виллонодулярный синовит
XII. Non-rheumatic diseases with arthropathy

1.0. allergic diseases
2.0. Metabolic disorders
2.1. Amyloidosis
2.2. Ochronosis
2.3. Hyperlipidemia
2.4. hemochromatosis
3.0. Congenital defects of the connective tissue metabolism
3.1. Marfan's syndrome
3.2. Desmogenez imperfecta (Ehlers - Danlos syndrome)
3.3. Hypermobility syndrome
3.4. MPS
Рабочая классификация и номенклатура
ревматических болезней (1999)

XII. Артропатии при неревматических
заболеваниях
1.0. Аллергические заболевания
 2.0. Метаболические нарушения 2.1. Амилоидоз 2.2.
Охроноз 2.3. Гиперлипидемия 2.4. Гемохроматоз
 3.0. Врожденные дефекты метаболизма
соединительной ткани 3.1. Синдром Марфана 3.2.
Десмогенез несовершенный (синдром Элерса —
Данло) 3.3. Синдром гипермобильности 3.4.
Мукополисахаридоз


4.0. endocrine diseases
5.0. nervous
6.0. Diseases of the blood
7.0. Paraneoplastic syndrome (malignant tumors of
various sites)
8.0. occupational diseases
9.0. Other diseases 9.1. Sarcoidosis is 9.2. Periodic
disease 9.3. Chronic active hepatitis 9.4.
hypovitaminosis C
 4.0.
Эндокринные заболевания
 5.0. Поражения нервной
 6.0. Болезни системы крови
 7.0. Паранеопластический синдром (при
злокачественных опухолях различной локализации)
 8.0. Профессиональные болезни
 9.0. Другие заболевания 9.1. Саркоидоз 9.2.
Периодическая болезнь 9.3. Хронический активный
гепатит 9.4. Гиповитаминоз С
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XIII. Diseases of the extra-articular soft tissues 1.0.
Diseases of the muscles of
1.1. Myositis
1.2. Ossifitsiruyuschy myositis
2.0. Diseases of the tissues around
3.0. Diseases of the fascia and aponeuroses 4.0,
subcutaneous disease. Fat
5.0. Poliosteoartromialgiya (psychogenic
rheumatism)
Рабочая классификация и номенклатура
ревматических болезней (1999)



XIII. Болезни внесуставных мягких тканей 1.0.
Болезни мышц 1.1. Миозиты 1.2.
Оссифицирующий миозит 2.0. Болезни
околосуставных тканей 3.0. Болезни фасций и
апоневрозов 4.0, Болезнь подкожной .жировой
клетчатки 5.0. Полиостеоартромиалгия
(психогенный ревматизм)

XIV. Bone disease and osteochondropathy
1.0. bone disease
1.1. Osteoporosis (osteopenia), generalized
1.2. osteomalacia
1.3. Osteopathy hypertrophic pulmonary (MarieBamberger syndrome)
1.4. Osteitis deformans (Paget's disease)
1.5. Osteolysis (unspecified etiology)


XIV. Болезни костей и Остеохондропатии
1.0. Болезни костей
 1.1.
Остеопороз (остеопения) генерализованный
 1.2. Остеомаляция
 1.3. Остеопатия гипертрофическая легочная (МариБамбергера синдром)
 1.4. Деформирующий остеит (болезнь Педжета)
 1.5. Остеолиз (неуточненной этиологии)

2.0. osteochondropathy
2.1. Aseptic necrosis of the femoral head (Perthes
disease) and other sites (Köhler's disease I and II,
disease Kenbeka, etc.)
2.2. osteochondritis dissecans
2.3. Osteochondropathy vertebral disease
(Sheyermana - May, Calve's disease)
2.4. Osteochondropathy tuberosity of the tibia
(Osgood disease - Schlatter

2.0. Остеохондропатии
 2.1.
Асептические некрозы головки бедренной
кости (болезнь Пертеса) и других локализаций
(болезнь Келера I и II, болезнь Кенбека и др.)
 2.2. Рассекающий остеохондрит
 2.3. Остеохондропатии тел позвонков (болезнь
Шейермана — May, болезнь Кальве)
 2.4. Остеохондропатии бугристости
большеберцовой кости (болезнь Осгуда —
Шлаттера
Laboratory studies
The values of laboratory data


Laboratory tests may help in diagnosis and to
confirm data obtained by history taking and
examination, but are not independently diagnostic
criteria.
In addition, laboratory tests can help monitoring
disease activity, but they are meaningful only when
correlated with clinical outcome.
Laboratory studies in rheumatic diseases

Anemia

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Leukocytes
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Leukocytosis - A high activity of inflammation, with Still, the infection
Leukopenia - SCR (lymphopenia), with m-Felty (neutropenia)
Platelets

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Normochromic - Correlation with disease activity
Iron - NSAID-associated gastrointestinal pathology
Hemolytic - SLE, APS
Aplastic - Citostatic, phenylbutazone, D-penicillamine, etc.
Thrombocytosis - The high activity of inflammation
Thrombocytopenia - SLE, APS
KLF - Increase - Inflammatory myopathies
Laboratory studies in rheumatic diseases


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Transaminases, bilirubin - Increase - Pathology of the liver with
"rheumatologic" manifestations of the toxicity of drugs
(methotrexate, NSAIDs)
Uric acid - Hyperuricemia – Gout
Markers of inflammation



Increased ESR - Active inflammation , a diagnostic criterion for
polymyalgia rheumatica and giant cell arteritis, intercurrent infection
Increased CRP - PA - activity of inflammation, joint destruction, SLE intercurrent infection
Uroscopy


Microhematuria – nephritidis (SLE, systemic vasculitis), toxic drugs
Proteinuria – nephritidis (SLE, systemic vasculitis, amyloidosis), the toxicity
of drugs
The value of immunological tests in rheumatic
diseases
Disease
Diagnosis in
tipical clinic
manifest
Dif-Diagnosis
Scrining
Monitoring
Anti-nuclear
SLE
+++
++
-
?
Anti-DNA
SLE
+++
+
-
+++
Anti-body -Sm,
RNP
SLE, Mixt
path
+++
+++
-
-
С3, С4
Nephrop
aties in
SLE
++
++
-
+++
СН50
SLE
+
+
-
+
Rheumatoid factor
RA
+++
+
?
+
Test
The value of immunological tests in rheumatic
diseases
Disease
Diagnosis in
tipical clinic
manifest
Dif-Diagnosis
Scrining
Monitoring
AR
+
+
-
+++
AR, SLE
+
-
?
+
АSL-0
ARF
++
++
-
+
ANCA
Vasculitidi
s
+++
++
-
+
APhS
+++
++
-
+
AS
++
-
-
-
Lyme d.
+++
++
-
+
Test
CRP
Cryoglobulins
Аnti-phosfolipides
HLA B-27
Anti-body at
Lyme
The disease, in which can increase the
RF in the serum
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Subacute bacterial endocarditis
Leprosy
Chronic inflammatory disease of unknown etiology
Tuberculosis
Syphilis
Sarcoidosis
Lyme Disease
Periodontal disease
Interstitial lung disease
Viral diseases
Liver disease
Rubella
Cytomegalovirus
Mixed cryoglobulinemia
Autoantibodies in rheumatic diseases
Type
Аnti –ds DNA
Anti – SSA/Ro
Description
Antibodies to double strand of
DNA, have greater specificity than
antibodies to ssDNA
Most diagnostic tools are not
shared by antibodies to the five
main types of histones
Typical
diagnosticum
to
2
extractable nuclear antibodies (Sm
and RNP - ribonucleoprotein)
ribonucleoprotein
Anti – SSB/La
ribonucleoprotein
Anti – Histon
Anti – ENA
Clinical interface
Highly specific for SLE, rarely detected
in other diseases and in healthy people
SLE, lupus medication, other autoimmune
diseases
Highly specific for SLE
SLE (especially subacute cutaneous
lupus), lupus neonatal syndrome
Shogren
Shogren's syndrome, lupus
erythematosus, SLE newborn
Autoantibodies in rheumatic diseases
Type
Anti –
centromer
Anti – Scl 70
Anti – Jo-1
Anti – PM-Scl
Anti – Mi-2
Description
Antibodies to the centromere /
kinetochore region of chromosome
Antibodies to topoisomerase 1 DNA
Antibodies to the transfer-RNA
synthetase
Clinical interface
Limited scleroderma (CREST)
scleroderma
Poly / dermatomyositis, particularly in
patients with insterstitsialnym lung
disease, Raynaud's phenomenon,
cracked skin of hands (mechanical arm),
arthritis, and resistance to therapy
Antibodies to nuclear components Polymyositis / scleroderma Overlap
of granular
syndrome
Antibodies to nuclear antigens of dermatomyositis
unknown function
The main indications for diagnostic arthrocentesis


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
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Monoartritis
Trauma with effusion into the joint cavity
Suspected purulent arthritis
Suspicion of microcrystalline (urate, hydroxyapatite),
arthritis
unclear diagnosis
The value of radiology in rheumatic diseases
Disease
Thorax
Hand and
foot
Sacroili
ac
Knee joints
other
Rheumatoid
arthritis
+
+++
+
+
The thoracic spine
Osteoarthritis
-
++
+++
+++
-
AS
-
-
+++
-
Lumbar spine
Reactive arthritis
-
++
+++
-
Heel bone
SLE
+++
++
++
-
-
Scleroderma
+++
++
-
-
The Esophagus
Gout
-
++
-
-
-
Osteoporosis
-
-
-
-
Densitometry, spine
Minimum set of laboratory tests to diagnose the causes of joint
pain

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The total blood count,
platelets
ESR
Bilirubin
Transaminase
CK
Creatinine
uric acid
Urinalysis, daily urine for protein
Microscopic analysis of synovial
fluid, including crystals

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CRP
rheumatoid factor
antinuclear factor
Anti-DNA
A/b to extractable nuclear
antigen (RNP)
ANCA
ASL-O
Determination of chlamydial
antigen
A/b to B.burgdorferi
HLA B-27
Minimum set of radiographic studies to
diagnose the causes of joint pain

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Chest
Hands and distal foot in front projection
Pelvis in frontal projection
Knee in frontal and lateral projections
Cervical spine in a straight line and lateral projections
The lumbar spine and lateral projections
Heel bone
Esophagus
Densitometry
Application of the morphological study (biopsy) in diagnosis of
rheumatic diseases and their complications

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Polymyositis
Sjogren's disease
Diffuse eosinophilic fasciitis
Systemic vasculitis
Secondary amyloidosis
Differential Diagnosis in subcutaneous sites (rheumatoid
nodule / tophi)
Differential diagnosis of suspected tumor of the synovial
Drugs used to treat rheumatic diseases
Non-steroidal anti-inflammatory drugs for treatment
of rheumatic diseases
Medication
Diclofenac potassium
Diclofenac sodium
Etodolak
Ibuprofen
Indomethacin
Ketoprofen
Meloxicam
Naproxen
Nimesulide
Piroxicam
Dose
100-200 mg/24 h, divided into 2-4 reception
100-200 mg/24 h, divided into 2-4, or 100 mg in
the form of retard
800-1200 mg/24 h, divided into 2-4 reception. In
the form of retard 1 dose 400-1000mg/24 h
1200-3200 mg/24 h, divided into 3-4 reception
50-200 mg/24 h, divided into 2-4, either in the
form of retard 75 mg 1 times a day, 75 mg 2
times daily
200-225 mg/24 h divided into 3-4 reception or
retard-150-200 mg/24 h 1 times
7.5 -15 mg/24 h 1 times per day
500-1500 mg/24 h divided 2 reception
100-200 mg/24 to 1-2 reception
20 mg/24 h in 1-2 reception
Possible side effects
For
all
abdominal
stomach,
discomfort,
(oedema),
nausea,
heartburn,
headache,
reactions
NSAIDS:
pain, or
cramps,
edema
diarrhea,
vomiting,
dizziness,
allergic
Prevention and treatment of GASTROINTESTINAL pathologies
resulting from receiving NSAIDS
•Antacids
•have no data about their effectiveness
•H2-blockers
•Cure duodenal injury duodenal injury in Warn high doses
were effective at the level of the stomach and eliminate
symptoms caused by NSAIDS
•Improve semiology
•Inhibitors proton pump
•is effective for the prevention and treatment of
gastroduodenal of defeats
•Improves semiology
Risk factors for the development of renal failure
in the application of NSAIDs
High risk
Reducing the volume of circulating blood, as significant bleeding or hemodynamic
disturbances on the type of shock
Severe heart failure
Cirrhosis of the liver with / without ascites
Clinically significant dehydration
Low - medium risk
True kidney disease
diabetic nephropathy
nephrotic syndrome
hypertensive nephropathy
beginning of anesthesia
The controversial risk
advanced age
Corticosteroids
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Corticosteroids are widely used in the treatment of
inflammatory forms of arthritis and related systemic
autoimmune diseases.
In addition to their strong anti-inflammatory effect, they
regulate a wide range of metabolic, immunological and
central nervous system function.
For systemic therapy have been issued numerous
synthetic derivatives, but the prednisone, prednisolone,
and methylprednisolone are used most widely.
Corticosteroids
Form
Hydrocortisone
Cortisone
Prednisone
Methylprednisolone
Prednisolone
Dexamethasone
Relative antiinflammatory
potential
1
0,8
4
5
5
20-30
Equivalent dose
(mg)
Elimination half-life
(h)
20
25
5
4
4
0,75
8-12
8-12
12-36
12-36
12-36
36-54
Side effects of long-term CorticoTherapy

Frequent
Hypertension
 Negative calcium balance and secondary
hyperparathyroidism
 Negative nitrogen balance
 Obesity, moon face, supraclavicular fat accumulation in
the area, fat accumulation in the form of a mountain on his
back,
 Slowing of wound healing, erythema face, thin, fragile
skin, blue striae, petechiae and ecchymosis
 Acne

Side effects of long-term Cortico-Therapy
Growth retardation in children
 Adrenal insufficiency, resulting in suppression of the
hypothalamic-pituitary-adrenal system
 Hyperglycemia, diabetes mellitus, dyslipidemia,
atherosclerosis
 Sodium retention, hypokalemia
 Increased risk of infection, neutrophilia, lymphopenia
 Osteoporosis, compression fractures of vertebrae,
Osteonecrosis
 Mood changes such as euphoria, emotional lability,
insomnia, depression, increased appetite
 subcapsular cataract

Side effects of long-term CorticoTherapy

medium frequency
metabolic alkalosis
 Diabetic ketoacidosis, hyperosmolar diabetic coma
 Peptic ulcer (usually the stomach), gastric bleeding
 "Silent" intestinal perforation
 Increased intraocular pressure and glaucoma
 Mild intracranial hypertension or pseudotumor of the brain
 spontaneous fractures
 psychosis

Side effects of long-term CorticoTherapy

Rare
Sudden death in the rapid introduction of high-dose, pulse
therapy
 Valvular damage in SLE
 In susceptible patients may develop heart failure
 Cellulitis (after cancellation)
 Hirsutism or virilism, impotence, secondary amenorrhea
 Hepatomegaly as a result of fatty liver
exophthalmos
 Allergies to synthetic corticosteroids (urticaria, angioedema)

Pathogenic (Basic) therapy of inflammatory
rheumatic diseases
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Disease modifying antirheumatic drugs (DMARDs) - the
basic drugs from diverse group of funds that reduce the
symptoms of rheumatoid arthritis (RA) and other
inflammatory autoimmune diseases.
In addition, there is increasing evidence that treatment
with DMARD, especially if appointed early in the course
of the disease, can delay the progression of cartilage
and bone.
When the RA is not responding to treatment DMARD,
can be applied biological therapy. Biologicals alter the
action of cytokines
Basic therapy
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When to start - an understanding that changes in the joints can occur
within the first 12 months of the debut of RA, led to the earlier
introduction of DMARD and more aggressive combination DMARD.
Monotherapy - Methotrexate is considered standard therapy for
DMARD.
Combination therapy - Join one or two DMARD therapy with
methotrexate for the background is often used in an attempt to
improve clinical response in those patients who did not give an
answer to monotherapy with methotrexate. The most commonly used
combinations of DMARD - "triple therapy" (methotrexate +
hydroxychloroquine sulfosalazin +) or methotrexate plus a biological
agent.
Pathogenetic (Basic) drugs
Medication
Azathioprine
Wobenzym
Cyclophosphamide
Cyclosporine
Hydroxychloroquine
Dosage
50-150 mg/day in 1-3
reception
Possible side effects
Leukopenia,
increased
transaminase
Flatulence, change the color
and smell of urine, rarely
15-9 drops in 3 reception
allergic reactions in the form
of urticaria
Hematuria,
hair
loss,
50-150 mg per day in single
leukopenia,
amenorrhea,
dose
nausea, vomiting
Hypertension, increased hair
100-400 mg daily in 2
growth,
reduced
kidney
reception
function, hypertrophy of gum,
tremor
200-600 mg daily in 2-1 Violation of, diarrhea, rash
reception
Pathogenetic (Basic) drugs
Medication
Leflunomid
Methotrexate
Mycophenolate
Mikofenolat
Sulfasalazine
Wobenzym
Dosage
Possible side effects
dizziness,
hair
loss,
10-20 mg/day in 1. Treatment Diarrhea,
begins with a dose of 100 mg hypertension, increased transaminase,
leukopenia, rash on the skin
support screens from 3
consecutive days
Discomfort in the stomach, skin rash,
headache, photosensitivity, increased
transaminase, leukopenia, ulcers in the
7.5-20 mg/week
mouth, weakness, fatigue
1.5-day
500-3000 mg daily in 2-4
reception
9-15 drops in 3 reception
Diarrhea, moderate leukopenia
Abdominal pain, diarrhea, increased
sensitivity, reduced appetite, nausea,
vomiting, rash on the skin
The feeling of crowding in the
stomach, nausea, allergies (skin
rashes).
Treatment strategies with drugs
1. Sequential monotherapy
2. Step-up (ascending) combination
therapy
3. Step-down (descending) combination
therapy
4. Combination with a biological agent
Biological therapy


One of the most important achievements of the
pharmacotherapy of inflammatory rheumatic
diseases associated with the development of
entirely new group of drugs, which are called
"biological" agents.
Their mechanism of action is associated with
suppression of synthesis of "inflammatory" cytokines,
play a fundamental role in the immunopathogenesis
of these diseases, especially RA.
Immunomodulating and proinflammatory effects of cytokines in
the pathogenesis of inflammatory rheumatic diseases (1)

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
Vascular endothelial cells - enhance the expression of
adhesion molecules (ISAM-1, VSAM-1, E-selectin) through the
activation of NF-kV stimulate angiogenesis, leading to
disruption of anticoagulant activity (stimulation of the synthesis
of tissue factor, suppression of synthesis of thrombomodulin).
Lymphocytes - contribute to the development of lymphoid
tissue, modification of SV44 and the ability to bind to the
ligand.
Dendritic cells - cells induce the maturation and migration from
nonlymphoid organs to secondary lymphocyte organs.
Neutrophils and platelets - contribute to activation.
Immunomodulating and proinflammatory effects of cytokines in
the pathogenesis of inflammatory rheumatic diseases (2)
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Fibroblasts and synoviocytes - lead to proliferation.
Pro-inflammatory cytokines - in addition induce the synthesis
of IL-1, IL-6, granulocyte-macrophage colony-stimulating
factor.
Other pro-inflammatory mediators - induce the synthesis of
PGE2 through activation of COX-2, leukotrienes, platelet
activating factor, nitric oxide and reactive oxygen species.
Metalloproteinases - induce the synthesis of collagenase,
gelatinase, stromelysin.
Other effects - increase pain, induce cachexia, induce fever,
mobilize calcium from the bones; modulate apoptosis.
Biological therapy



The particular interest is the use of monoclonal
antibodies.
These drugs have very high specificity, which provides a
selective effect on certain links in the
immunopathogenesis of disease, minimally affecting
normal functioning mechanisms of the immune system.
This can significantly reduce the risk of "generalized"
imunosupresed, which is typical of many drugs,
especially glucocorticoids and cytotoxic drugs.
Monoclonal antibody to TNF-α
Hummanised
Humman
Kimerik
Mouse
100% human protein
5% -10% protein of the
mouse
25% protein of the
mouse
100% mouse protein
Infliximab
Adalimumab
Adalimumab
Golimumab
(Adalimumab)
Biological therapy

The main target for anticytokine monoclonal
antibody therapy is:
 TNF-alpha
(infliximab, adalimumab, etc.)
 IL-6 (tocilizumab)
 CD20 B cells (rituximab)
 IL-1, IL-2, etc.
Contraindications of biological
therapy
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
Congestive heart failure,
Severe infection
Latent tuberculosis
Malignant neoplasms
Pregnancy and lactation.
Biologicals
Corticosteroids
Basic drugs
(methotrexate, sulfasalazine, leflunomid)
The number of patients
The gravity of the condition of the
patient
The need for biological specimens
THANK YOU!
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What is Rheumatology?
Rheumatology is the non-surgical subspecialty of internal medicine that
focuses on common and complex problems that may affect the entire body,
and frequently involves the musculoskeletal system. Such diseases include:
rheumatoid arthritis; gout; lupus; scleroderma; osteoporosis;
fibromyalgia and spondylitis. Common problems such as
tendonitis, back pain, bursitis and carpel tunnel syndrome can
be a result of rheumatologic disorders as well.
There are more than 100 types of rheumatological disorders,
some of which are very serious and difficult to diagnose and
treat.