Transcript Slide 1

Children’s Oncology Group
Sarcoma Plans
Holcombe E. Grier MD
For the Children’s Oncology Group
Lots of Folks Involved
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Bone Sarcoma Committee
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Neyssa Marina- chair
Rich Gorlick- vice chair
Mark Bernstein- previous chair of bone sarcoma
committee
Mark Krailo- biostatistician
Soft Tissue Sarcoma Committee
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William Meyer- chair
Doug Hawkins- vice chair
James Anderson- biostatistician
Plan: Present Upfront and Relapsed
Trials for Following Diseases
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Bone tumors
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Osteosarcoma
Ewing Sarcoma
Soft Tissue Sarcomas
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Rhabdomyosarcoma
Non-Rhabo STS
Infantile fibrosarcoma
Desmoid tumor
Osteosarcoma: Up front trials
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Patients without metastases: Euramos
(Neyssa Marina USA chair)
Metastatic:
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Recently completed trial of feasibility of adding
transtuzumab (herceptan) to MAP (David Ebb)
Plan to incorporate bisphosfonates
(zolendronic acid) into MAP background
Osteosarcoma-Treatment at First Pulmonary
Relapse: Inhaled GM-CSF (Arndt PI)
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For patients with
bilateral mets
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Resect one side
2 cycles GM-CSF
Resect other sidemeasure Fas/FasL in
tumor
Also using for patients
with unilateral disease
Disease free interval
will be measured
Ewing Sarcoma: Upfront treatment
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Patients without metastases
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Still analyzing dose compression trial (Rick
Womer)
Next trial will incorporate
topotecan/cyclophosphamide pair (Mason
Bond)
Patients with metastases
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EuroEwings: pulmonary mets (Doug Hawkins)
Metranomic therapy (Judy Felgenhauer)
Schema: AEWS0031
(Mason Bond)
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VAdCA
alt with
I/E
Duration 48 weeks
VAdCA
alt with
I/E
alt with
V/T/C
Duration 48 weeks
Metronomic Therapy for Patients Presenting
with Extensive Metastases
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PI Felgenhauer
Standard therapy backbone (Vcr, Dox, Cyclophos
alt with ifosfamide/etoposide)
Overlay of
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Celecoxib 250 mg/m2 per day
Vinblastine 1 mg/m2 three times weekly
Objective is feasibility of regimen, estimation of
EFS, assessment of surrogate angiogen. markers
Will reach accrual soon
Concept for Next Trial for Patients
with Extensive Metastases
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Pilot to look at addition of
irinotecan/temozolomide to standard
therapy
Goal will be feasibility
Also considering bevacizumab
randomization
Rhabdomyosarcoma-Up Front
Patients Without Metastases
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Low Risk (David Waterhouse PI) Emb only
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4 courses VAC for all patients; Subset A stops
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4 more VA courses for subset B
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Stage 1, clinical group I/II & orbital group III, stage 2
clinical group I, II
Stage 1, group III not orbit or stage 3 clinical group I/II
Intermediate risk (Doug Hawkins PI)
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Randomize VAC vs VAC alternating with
Vincristine/Irinotecan
Rhabdomyosarcoma
Patients Presenting with Metastases
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Brenda Weigel PI
Intensive regimen
Rx
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Vincristine, irinotecan window
VDC
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Iriniotecan/vcr during radiation
NRSTS
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NRSTS: Risk based rx, Sherry Spunt PI
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Infantile fibrosarcoma, Mignon Loh PI
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7 cycles ID
VAC, stopping C before infertility likely
Convert non-operable to operable
Desmoid tumors, Steve Skapek PI
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f/u to mtx/vbl study
Sulindac and tamoxifen
Biology Trials
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Collecting specimens at diagnosis for each
tumor type
Collection process has been extremely
successful
Committees review concepts for use of the
tissue