Transcript Slide 1
Palliative Care of Respiratory Symptoms James S. Botts, MD, FACP Southwest Area Medical Director VistaCare Outline of Topics… Identification of the Patient with Endstage Pulmonary Disease Dyspnea Cough Pulmonary Infections Hemoptysis Pulmonary Hypertension and Cor pulmonale Primary Pulmonary Hypertension Pulmonary Fibrosis Pulmonary Emboli Stridor Neuromuscular Disorders & Restrictive Pulmonary Disease Bronchiectasis and Cystic Fibrosis α-1 Antitrypsin Deficiency List of Links 2 Identification of Endstage Pulmonary Disease No single event or parameter signals end stage Persistent dyspnea despite optimal medical treatment Dyspnea impairing efforts to leave home Increasing number of hospital admissions Limited improvement after hospitalization Increasing number of physician visits Onset of fear, anxiety or panic attacks Expression of concerns about dying No reference to oxygen saturation or other parameter of pulmonary function It is difficult to accurately identify those with a prognosis of six months or less 1. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 903 3 Identification of Endstage Pulmonary Disease Using CMS LCD pulmonary guidelines 50% of patients qualifying for pulmonary disease will live six months or less (n = 94)* Pulse rate > 100 has the best correlation with a prognosis of six months or less in patients with endstage pulmonary disease 65.38% of patients meeting the CMS LCD guidelines for pulmonary disease with a pulse rate > 100 will live less than six months (n = 29)* * Hospice Eligibility Evaluation Database (HEED) ; J.S. Botts 4 Palliative Care of Dyspnea Main Menu… Palliative Care of Dyspnea Definition of Dyspnea (American Thoracic Society) “A subjective experience of breathing discomfort consisting of qualitatively distinct sensations that vary in intensity. Physiologic, psychologic and environmental factors all may play a role. The severity varies widely among patients.”(2) 2. American Journal of Respiratory and Critical Care Medicine - Jan 1999 ARS-1 6 Palliative Care of Dyspnea Correlation of the complaint with the pathology of the underlying disease. Little correlation in general Some correlation of the following: “I am drowning.” – Pulmonary edema with CHF “I can’t get enough air in.” – Interstitial disease or pulmonary emboli.(2,3) “Tight”, “Constricted” – a sensation used by those with airways obstruction such as asthma and cystic fibrosis but not COPD 2. Chest. 2005;127:1877-1878 3. Excerpt: Chest. 2005;127:1877-1878 7 Adapted From: Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 898 Motor Cortex Peripheral Chemoreceptors Sensory Cortex Emotions Personality Aorta and Carotid Arteries Dyspnea Central Chemoreceptors Medulla Sense levels of oxygen, carbon dioxide and pH of the blood. Midbrain Respiratory Center Sense levels of oxygen, carbon dioxide and pH of the blood. Mechanoreceptors Lungs and Chest Wall Respiratory Muscles of Breathing Sense stretching of structures in lungs and chest wall Pathophysiology of Dyspnea 9 Palliative Care of Dyspnea Assessment of Dyspnea Five etiologic categories Cardiac Pulmonary Neuromuscular Psychiatric / Social / Spiritual Any combination of the above 10 Palliative Care of Dyspnea Assessment of Dyspnea History and Physical Examination Frequently identifies the specific system responsible for the dyspnea Indicated diagnostic testing follows 11 Palliative Care of Dyspnea Assessment of Dyspnea - Testing Pulmonary Testing ABG Chest X-ray Pulmonary Functions Bronchial Challenge High resolution CT Lung scan PET Diaphragmatic Fluoroscopy Cardiac Testing EKG Echocardiography Coronary angiography Myocardial perfusion scan Other Sleep studies Esophageal pH monitoring Laryngoscopy Often hospice and palliative care patients choose not to be tested, placing more reliance on the history and physical examination. 12 Palliative Care of Dyspnea Assessment of Dyspnea Reporting Intensity of Dyspnea Verbal numerical scales (0-10) VAS (Visual Analog Scale) Modified Borg Dyspnea Scale Link to Modified Borg Dyspnea Scale 13 Palliative Care of Dyspnea Assessment of Dyspnea Common Physiological Measurements of Respiratory Disease Spirometry FEV1 is a POOR predictor of dyspnea and improvements in dyspnea after bronchodilators do not match improvements of FEV1(4,5) Oxygen saturation – with its limitations(6) NOT a good predictor of the subjective feeling of dyspnea 4. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 5. Lareau, S.C. et al. (1999).Dyspnea in patients with chronic obstructive pulmonary disease: does dyspnea worsen longitudinally in the presence of declining lung function? Heart & Lung 28 65-73 6. eMedicine - Pulmonary Function Testing : Article by Raed A Dweik, MD, FACP, FCCP, FRCPC 15 Palliative Care of Dyspnea Treatment – Non-Pharmacologic Influenza and pneumonia vaccines Cold facial stimulation (i.e. fan)(6) Nutrition(7) Weight gain for malnourished COPD (“pink puffer”) Weight reduction is accompanied by respiratory muscle weakness. Non-fluid weight gain will help correct this Weight gain is difficult to achieve – poor response to nutritional supplements Weight loss for hypercapnic COPD (“blue bloater”) 6. Am Rev Respir Dis. 1987 Jul;136(1):58-61 7. Am Rev Respir Dis. 1990 Aug;142(2):283-8. 16 Palliative Care of Dyspnea Treatment – Non-Pharmacologic Controlled cough Forced expiration – incentive spirometry Deep breath followed by coughing For clearing secretions Good for prevention and treatment of atelectasis Follow with controlled cough to clear secretions Emotional, spiritual and social counselling These issues are important just as they are in the control of pain Addressing these factors may improve the sensation of dyspnea 8. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 17 Palliative Care of Dyspnea Treatment – Non-Pharmacologic Exercise(8) Exercise is the best way to strengthen the respiratory muscles Methods Walking; stair climbing; Upper extremity and shoulder girdle strengthening These are accessory muscles of breathing Pulmonary rehabilitation Inspiratory resistance breathing No better than general reconditioning exercise alone in COPD patients 8. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 18 Palliative Care of Dyspnea Treatment – Non-Pharmacologic Controlled Breathing(8) Purse Improves alveolar ventilation and gas exchange Slow lipped breathing expiration Useful in overcoming associated panic attacks Bending forward position Improves diaphragmatic function through increasing intraabdominal pressure Helps relieve dyspnea 8. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 19 Palliative Care of Dyspnea Treatment – Non-Pharmacologic BiPAP (Bilevel Positive Airways Pressure) Reduces time in ICU Reduces need for intubation Reduces mortality in COPD exacerbations Improves quality of life in ALS patients (64) Value of BiPAP in a skilled care setting to “rest” the respiratory muscles is uncertain 8. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 64. Neurology. 2003 Jul 22;61(2):171-7 20 Palliative Care of Dyspnea Treatment – Non-Pharmacologic Summary… Immediate treatment Cold facial stimulation with a fan Controlled cough Forced expiration Pursed lip breathing Slow expiration Bend forward posture Non-immediate treatment Vaccinations – influenza & pneumococcal Nutritional assessment and treatment Addressing emotional, social and spiritual issues Exercise – walking; stair climbing; shoulder girdle strengthening 21 Palliative Care of Dyspnea Treatment – Pharmacologic Bronchodilators Antiinflammatories Oxygen Anxiolytics ARS-2 Mucolytics Antidepressants Antibiotics 22 Palliative Care of Dyspnea Treatment – Pharmacologic - Bronchodilators β2 agonists – in COPD Do not necessarily improve FEV1 or FVC Do improve dyspnea Anticholinergics Improve FEV1 Reduce dyspnea Phosphodiesterase Inhibitors Theophylline Leukotriene Antagonists 23 Palliative Care of Dyspnea Treatment – Pharmacologic - Bronchodilators β2 agonists In stable COPD Short acting levalbuterol (Xopenex®) – In stable COPD patients, no advantage over racemic mixture (albuterol) in prn doses(9) Long acting β2 agonists salmeterol (Serevent®), formoterol (Foradil®), arformoterol (Brovana®) 9. Chest. 2003 Sep;124(3):844-9 24 Palliative Care of Dyspnea Treatment – Pharmacologic - Bronchodilators Anticholinergics Short acting – Ipratropium (Atrovent®) Long acting Tiotropium (Spiriva®) Tiotropium (Spiriva®) alone is more effective than long acting β2 agonists alone in COPD patients (10) Tiotropium (Spiriva®) added to a regimen of a long acting β2 agonist and a corticosteroid significantly improved dyspnea, FEV1 and FVC in COPD patients(11) Comparing tiotropium alone to fluticasone/salmeterol/tiotropium therapy showed no difference in rates of COPD exacerbation but the combination therapy did improve lung function, quality of life, and hospitalization rates in patients with moderate to severe COPD.(11a) 10. Thorax. 2003 May;58(5):399-404 11. Respirology. 2006 Sep;11(5):598-602 11a. Annals of Internal Medicine. 2007 April 17; 146( 8):545-555 25 Palliative Care of Dyspnea Treatment – Pharmacologic - Bronchodilators Theophylline(12) A non-selective phosphodiesterase (PDE) inhibitor with antiinflammatory and bronchodilatory effects Improves dyspnea Improves FEV1 24 hour sustained release preparation may be given once before bedtime without disturbing sleep (13) Is now used less because of narrow therapeutic range and risks of toxicity. ? Resurgence due to antiinflammatory effects and lower serum levels (<10mg/L).(35a) On the horizon, “Cilomilast and roflumilast are selective PDE4 inhibitors that are currently in pre-registration and phase III clinical trials, respectively, for the treatment of COPD (cilomilast and roflumilast) and for treatment of asthma (roflumilast).”(35) 12. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 903 13. Chest, Vol 110, 648-653 35. Curr Opin Investig Drugs. 2006 May;7(5):412-7 35a. American Journal of Respiratory and Critical Care Medicine Vol. 167. pp. 813-818, (2003) 26 Palliative Care of Dyspnea Treatment – Pharmacologic - Bronchodilators Leukotriene Receptor Antagonists Zafirlukast (Accolade®)– Has bronchodilation effect in COPD and asthma There is no additive effect when added to inhaled steroids (34) May reduce pulmonary hypertension in COPD(35) Montelukast (Singulair®) There is long term benefit in elderly COPD patients with moderate to severe disease(36) 34. Pulm Pharmacol Ther. 2000;13(6):301-5 35. Chin Med J (Engl). 2003 Mar;116(3):459-61 36. Respir Med. 2004 Feb;98(2):134-8 27 Palliative Care of Dyspnea Treatment – Pharmacologic - Antiinflammatories Corticosteroids in the treatment of COPD / Dyspnea Short term oral corticosteroids: Acute exacerbation of COPD Long term inhaled corticosteroids: Reduces all cause mortality in moderate to severe COPD(14) Not a first line drug in mild COPD(15) Long term oral corticosteroids: Only in those not responding to inhaled corticosteroids Sometimes beneficial in hospice patients with malnutrition Identification of those who will benefit from long term use: Remains controversial One method: Check FEV1 then give a trial of 20-40 mg prednisone per day for 14 days, then repeat the FEV1. A ≥ 20% increase indicates the patient will benefit from inhaled steroids(16) 14. Thorax. 2005 Dec;60(12):992-7. Epub 2005 Oct 14 15. Curr Opin Pulm Med. 2004 Mar;10(2):113-9 16. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 903 28 Palliative Care of Dyspnea Treatment – Pharmacologic - Antiinflammatories Nebulized Indomethacin May be of value in reduction of mucus secretions in bronchiectasis and chronic bronchitis(52,53) Inhibits production of a proteolytic enzyme, neutrophil elastase May have long term beneficial effect on progression of bronchiectasis Dyspnea was improved(52) 52. Am Rev Respir Dis. 1992 Mar;145(3):548-52 53. Eur Respir J. 1995 Sep;8(9):1479-87 29 Palliative Care of Dyspnea Treatment – Pharmacologic - Oxygen Indications O2 saturation ≤ 89% with or without dyspnea Those with dyspnea relieved by O2 despite the resting oxygen saturation. Resting Studies have shown ↑ survival with use of long term oxygen, as well as improvement in health related quality of life measures including dyspnea (17,18) The level of O2 saturation does not correlate with the degree of dyspnea (17) 17. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 903 18. Curr Opin Pulm Med. 2004 Mar;10(2):120-7 30 Palliative Care of Dyspnea Treatment – Pharmacologic - Oxygen Beware! Patients on oxygen with high oxygen saturation and confusion or lethargy may have C02 retention Treat with discontinuation or reduction in oxygen flow and close observation Titrate to the flow of oxygen that does not cause the confusion or lethargy 31 Palliative Care of Dyspnea Treatment – Pharmacologic - Opioids Meta-analysis concludes that opioids in modest doses are effective in treating dyspnea(28) Dose – as little as 2.5 mg of MS q4h(29) Sustained release morphine reduces dyspnea(27) (Don’t start on the sustained release forms.) 27. BMJ. 2003 Sep 6;327(7414):523-8 28. Thorax. 2002 Nov;57(11):939-44 29. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 32 Palliative Care of Dyspnea Treatment – Pharmacologic - Opioids No clear evidence that inhaled morphine is effective in the relief of dyspnea(30) 30. Eur Respir J. 1997 May;10(5):1079-83 33 Palliative Care of Dyspnea Treatment – Pharmacologic - Anxiolytics Benzodiazepines Scant literature on the use of benzodiazepines in the treatment of dyspnea but they are commonly used (19, 20) Opioids are first line anxiolytic drugs for dyspnea secondary to advanced disease of any cause(21) 19. Q J Med. 1980 Winter;49(193):9-20 20. Am J Hosp Palliat Care. 1998 Nov-Dec;15(6):322-30 21. Can Fam Physician. 2003 Dec;49:1611-6. 34 Palliative Care of Dyspnea Treatment – Pharmacologic - Anxiolytics Buspirone (BuSpar®) Conflicting reports of its effect on dyspnea(22,23) Concerns about respiratory depression in COPD patients receiving anxiolytics is unfounded.(24) Anxiolytics can be beneficial in some patients with dyspnea, even those without appreciable anxiety.(24) 22. Respiration. 1993;60(4):216-20 23. Chest. 1993 Mar;103(3):800-4 24. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 35 Palliative Care of Dyspnea Treatment – Pharmacologic - Mucolytics N-Acetylcysteine (Mucomyst®) by mouth or inhalation will help patients with excessive or viscous mucous clear these secretions Effect on dyspnea has not been studied Evidence is conflicting as to its reduction of COPD exacerbations(31,32) 31. Lancet. 2005 Apr 30-May 6;365(9470):1552-60 32. Eur Respir J. 2003 May;21(5):795-8 36 Palliative Care of Dyspnea Treatment – Pharmacologic - Mucolytics Additional agents that may assist in mucolysis and expectoration of thick sputum: Normal or hypertonic saline nebulizations Inhaled mannitol powder (66) Inhaled atropine Corticosteroids β2 agonists Indomethacin Theophylline Glycerol guaiacolate Of limited value 33. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 66. Respirology. 2005 Jan;10(1):46-56 37 Palliative Care of Dyspnea Treatment – Pharmacologic - Antidepressants SSRIs; Tricyclics – In depressed patients with endstage lung disease Beneficial for anxiety Benefit for dyspnea is not conclusive (25,26) 25. Psychosomatics. 1998 Jan-Feb;39(1):24-9. 26. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 904 38 Palliative Care of Dyspnea Treatment – Pharmacologic - Antibiotics Treatment of Exacerbations Antibiotics Fluoroquinolones (37,38) Amoxicillin almost as effective and cheaper(39) acting β2 agonists → long acting Short acting anticholinergics → long acting Oral prednisone → Inhaled corticosteroid Short 37. Clin Microbiol Infect. 2006 May;12 Suppl 3:42-54 38. Chest. 2004 Mar;125(3):953-64 39. American Family Physician Vol. 70/No. 4 (August 15, 2004) 39 Palliative Treatment of Cough Main Menu… Palliative Care of Cough Assessment Many patients will not want the usual diagnostic tests A thorough history and physical examination is often our best and only tool for assessing the cause of the cough ARS-3 41 Palliative Care of Cough Assessment Causes Acute infections Chronic Infections Airways Disease Cardiovascular Parenchymal Disease Irritant Recurrent Aspiration Drug Induced Pleural Disease Vocal Cord Disease Examples Pneumonia; Acute Bronchitis Chronic bronchitis; Bronchiectasis COPD; Asthma LV failure; pulmonary edema Interstitial Fibrosis GERD; Foreign body Stroke; Motor neuron disease ACE Inhibitors; inhaled drugs Pneumothorax; pleural effusion Paralysis; nodules on cords 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 42 Palliative Care of Cough Treatment of the Underlying Cause Acute and chronic infections Diuretics, ACE inhibitors, ± βblockers Recurrent aspiration Postioning of patient; swallowing evaluation → alter food consistency ENT evaluation and treatment GERD Correct pneumothorax; drain pleural effusion Vocal cord dysfunction Discontinue drug Pleural disease Bronchodilators and antiinflammatories Left ventricular failure Drug induced (ACE inhibitors) Antibiotics Asthma and COPD PPIs; metoclopramide; positioning of patient Post-nasal drip Decongestants; antihistamines 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 43 Palliative Care of Cough Treatment – Protussive and Antitussive Protussive Treatments Measures to improve cough effectiveness and secretion clearance Antitussive Treatments Measures to prevent or eliminate cough 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 44 Palliative Care of Cough Treatment – Protussive Treatments Measures to make cough more effective(40) hydration – po fluids; steam inhalations; saline nebulizations Physiotherapy – only in select patients with COPD and bronchiectasis (41) Adequate Forced exhalations Airways vibrations Postural drainage Assisted cough techniques 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 41. Chron Respir Dis. 2006;3(2):83-91 45 Palliative Care of Cough Treatment – Protussive Treatments Measures to make cough more effective(40) Pharyngeal suctioning Mini-tracheostomy For thick, excessive, infected sputum Steroids Antibiotics Inhaled mannitol powder or hypertonic saline (42,43) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 899 42. Cochrane Database Syst Rev. 2005 Jul 20;(3):CD001506 43. J Aerosol Med. 2002 Fall;15(3):331-41 46 Palliative Care of Cough Treatment – Protussive Treatments Increase of secretion clearance (40,44) Liquification of secretions N-acetylcysteine Recombinant human DNAse Arginine – not as effective as N-acetylcysteine Uridine-5'-triphosphate – useful for getting sputum samples from mild chronic bronchitics (67) Bronchodilators β2 – agonists (albuterol) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 900 44. Expert Opin Pharmacother. 2004 Feb;5(2):369-77 67. Chest. 2002 Dec;122(6):2021-9 47 Palliative Care of Cough Treatment – Antitussive Treatments Antitussive Treatment Used when cough is not reversible Used primarily for dry non-productive cough Opioids Oral local anesthetics Nebulized local anesthetics Other antitussive agents Antimuscarinics 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 900 48 Antitussive Treatment of Cough ACP Medicine 2006 ARS-4 49 Palliative Care of Cough Treatment – Antitussive Treatments Opioids Morphine Useful especially in the terminal patient Codeine is the strongest antitussive (47) is used widely In its OTC form codeine has no more antitussive effect than the demulcent vehicle (47) Dextromethorphan – an opioid derivative No analgesic effect in antitussive doses As effective as codeine for cough suppression 45. Chest. 2006 Jan;129(1 Suppl):284S-286S 46. Pulm Pharmacol Ther. 2004;17(6):459-62 47. Thorax. 2004 May;59(5):438-40 50 Palliative Care of Cough Treatment – Antitussive Treatments Oral Local Anesthetics Benzonatate (Tessalon Perles ®) Peripheral acting / opiates largely central acting Often effective in opiate resistant cough (47) Levodropropizine – not available in USA Widely used in Europe Peripheral acting and useful in cancer related cough (47) 45. Chest. 2006 Jan;129(1 Suppl):284S-286S 46. Pulm Pharmacol Ther. 2004;17(6):459-62 47. Thorax. 2004 May;59(5):438-40 51 Palliative Care of Cough Treatment – Antitussive Treatments Nebulized Local Anesthetics Risk is aspiration 2-4 hours after a treatment Patient should not eat or drink for 1 hour after Rx Nebulized lidocaine is effective in reduction of cough (48, 49) (5mg/kg in normal saline) Bupivacaine and Lidocaine have been associated with bronchoconstriction in patients with reactive airways. Consider giving with salmeterol (50) 48. Am J Emerg Med. 2001 May;19(3):206-7 49. Emerg Med J. 2005 Jun;22(6):429-32 50. Canadian Family Physician. May 2002 52 Palliative Care of Cough Treatment – Antitussive Treatments Other Antitussive Agents If cause is bronchospasm, inflammation, or tumor… Theophylline β2 –agonists Anti-inflammatories Steroids Sodium cromoglycate 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 53 Palliative Care of Cough Treatment – Antitussive Treatments Other Antitussive Agents OTC Marketed as Antitussive but Not Proven Effective Pseudoephedrine Dexbrompheniramine Guaifenesin 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 54 Palliative Care of Cough Treatment – Antitussive Treatments Antimuscarinics Ipratropium bromide Good in chronic bronchitis Reduces secretions without reduction in mucus viscosity Hyoscine .2-.4mg sc prn or Glycopyrronium bromide .2-.4 mg IM prn Good for the death rattle and associated cough May cause ataxia and hallucinations in the elderly 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 55 Palliative Care of Cough Treatment – Antitussive Treatments Antimuscarinics (68) Ophthalmic Atropine 1% drops Give sublingually or po Scopolamine Patch ® Hyoscine in a patch Not effective for about 12 hours 68. AAHPC Fast Fact and Concept #109: Death rattle and oral secretions 56 Palliative Care of Respiratory Infections Main Menu… Palliative Care of Respiratory Infections Treatment – Establishing Goals Above all - goals must be discussed and formulated with the patient and family The patient or POA may ultimately decide against antibiotic therapy If antibiotics are not chosen as a treatment, symptomatic treatment of fever, dyspnea and cough should be the plan 58 Palliative Care of Respiratory Infections Treatment – Antibiotic Selection COPD with FEV1 < 50% (Most hospice patients with end stage lung disease) exacerbations should be treated with a quinolone COPD with FEV1 > 50% use ampicillin, tetracycline or trimethoprim/sulfa 51. ACP Medicine Chapter 14:Respiratory Medicine: III Chronic Obstructive Disease of the Lung 59 Palliative Care of Respiratory Infections Treatment – Antibiotic Selection Bronchiectasis and Cystic Fibrosis Coverage of anaerobic bacteria and pseudomonas are important Antibiotics should be given in high doses, sometimes rotated and for 3-4 week courses Ciprofloxacin Metronidazole Augmentin 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 60 Palliative Care of Respiratory Infections Treatment – Antibiotic Selection Bronchiectasis and Cystic Fibrosis Nebulized antibiotics Gentamicin (300 mg bid) Tobramycin (300 mg bid) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 61 Palliative Care of Hemoptysis Main Menu… Palliative Treatment of Hemoptysis Assessment Majority of cases are mild to moderate <20% are massive (> 500 cc per day) Most common causes Infection ~ 80% TB Abscesses Bronchiectasis Malignancy ~ 20% 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 63 Palliative Treatment of Hemoptysis Assessment History and Physical Examination Examination of the sputum Presence of food particles Purulent sputum Hematemesis T/E fistula Infection Laboratory and X-Ray Studies Chest x-ray CT with contrast Bronchial artery or pulmonary artery arteriogram 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 64 Palliative Treatment of Hemoptysis Treatment - Anticipatory Anticipation - If resuscitation is or is not the goal Education of patient, family and caregivers Goals must be established Dark colored towels Morphine Anxiolytics Lorazepam Diazepam Midazolam 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 65 Palliative Treatment of Hemoptysis Treatment of Massive Hemoptysis If resuscitation is the goal… Patent airway + oxygen Intubation and ventilation if needed Position Lateral decubitus Head down Bleeding lung down Determine the site of bleeding Avoid excessive manipulation Cough suppression (codeine 30-60 mg po q6h) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 66 Palliative Treatment of Hemoptysis Treatment of Massive Hemoptysis – Goal Resuscitation If resuscitation is the goal…(continued) Immediate bronchoscopy If source identified, lavage with iced saline and adrenalin (10cc of 1:10,000 dilution) Topical thrombin Balloon catheter tamponade Vasopressin Bronchial stent placement If source not found CT with contrast Bronchial or pulmonary angiography 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 67 Palliative Treatment of Hemoptysis Treatment of Massive Hemoptysis – Goal Resuscitation If resuscitation is the goal…(continued) Bronchial arterial embolization Successful in 70-100% of cases Especially good in those with dilated bronchial arteries (bronchiectasis) Complications Rebleeding - common Anterior spinal artery infarction and paraplegia – 5% Ischemic necrosis of the bronchus Arterial dissection Surgical resection of the bleeding tissue 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 901 68 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Main Menu… Palliative Care of Pulmonary Hypertension and Cor Pulmonale Clinical Manifestations Dependent edema Right ventricular hypertrophy Right ventricular dilatation ARS-5 70 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Etiology and Pathophysiology Most chronic pulmonary diseases can ultimately cause pulmonary hypertension and cor pulmonale Pathophysiology (56) COPD – severe pulmonary hypertension only in a small percentage of COPD patients Hypoxia → constriction of pulmonary arterial vasculature – However… Chronic inflammation Repeated hyperinflation of the lungs Cigarette smoking Pulmonary Emboli and Pulmonary Fibrosis Poor correlation between arterial p02 and pulmonary artery pressure in COPD Obstruction of the pulmonary vasculature Primary Pulmonary Hypertension Etiology unknown 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 909 56. The Proceedings of the American Thoracic Society 2:20-22 (2005) 71 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Pathophysiology Pathophysiology of Edema in COPD Exercise → ↑ right ventricular end diastolic pressure → ↑ stretching of the right atrium → ↑ sympathetic tone → ↑ renin angiotensin aldosterone production → ↑ renal distal tubular retention of water and sodium → ↑ edema (56) C02 retention → ↑ renal proximal tubular sodium retention → ↑ edema 56. The Proceedings of the American Thoracic Society 2:20-22 (2005) 72 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Treatment Treat the underlying pulmonary disease Oxygen Long In term oxygen therapy in COPD Only produces a small decrease in pulmonary artery pressure acute exacerbations of COPD Delivered with BiPAP , reduces pulmonary artery pressure 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 909 73 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Treatment β2 – agonists Reduce pulmonary artery pressure Increase right ventricular ejection fraction Diuretics – the primary treatment of edema Edema is secondary to – Hypoxic renal dysfunction Excessive release of pituitary hormones Not caused by right heart failure Caution: hypochloremic alkalosis → ↓ ventilation and C02 retention Calcium Channel Blockers Only short term effect on pulmonary hypertension May produce ventilation-perfusion mismatch and worsen oxygen saturation May produce systemic hypotension 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 909 74 Palliative Care of Pulmonary Hypertension and Cor Pulmonale Treatment ACE Inhibitors Cause systemic hypotension No improvement in pulmonary vascular resistance, gas exchange or ventilatory parameters 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 909 75 Palliative Care of Primary Pulmonary Hypertension Main Menu… Palliative Care of Primary Pulmonary Hypertension Treatment Endothelin antagonists Bosentan Oral endothelin receptor blocker Mild improvement in dyspnea 36 meter increase in 6 minute walking distance (Tracleer®) (57) – Approved for use in pulmonary arterial hypertension May be used in patients with COPD and severe pulmonary hypertension, but these patients are difficult to identify in an end of life setting. Clinical trials are ongoing.(58) Caution – Numerous drug interactions 57. U.S. Pharmacist Vol. No: 30:05 Posted: 5/16/05 58. Curr Opin Pulm Med. 2003 Mar;9(2):139-43 77 Palliative Care of Primary Pulmonary Hypertension Treatment Prostacyclin Analogs Epoprostenol (Flolan®) and Treprostinil (Remodulin®) Improves exercise tolerance Must be given as a continuous infusion Iloprost (Ventavis®) Inhaled Improves exercise tolerance Beraprost – Not available in Inhaled Improvement in symptoms 57. U.S. Pharmacist Vol. No: 30:05 Posted: 5/16/05 USA 78 Palliative Care of Primary Pulmonary Hypertension Treatment Phosphodiesterase V Inhibitors Sildenafil (Viagra®) Improves exercise tolerance Other phosphodiesterase V inhibitors are being evaluated Tadalafil (Cialis®) – only once daily dosing Anticoagulants Warfarin – To prevent microthrombi formation in pulmonary circulation To prevent thrombophlebitis in the lower extremities Keep INR at 1.5 - 2.5 Reduces progression of the disease and those symptoms that will worsen with progression of the disease 57. U.S. Pharmacist Vol. No: 30:05 Posted: 5/16/05 79 Palliative Care of Pulmonary Fibrosis Main Menu… Palliative Care of Pulmonary Fibrosis Treatment Pneumoconioses – Most Common Cause Idiopathic Pulmonary Fibrosis Treatment with interferon gamma-1b Conflicting evidence of effectiveness (59,60) Metaanalysis suggests it does prolong life ( 61) In general pulmonary fibrosis patients do not retain CO2 High flows of oxygen may be used 59. Mayo Clin Proc. 2003 Sep;78(9):1082-7 60. Ann Pharmacother. 2005 Oct;39(10):1678-86. Epub 2005 Sep 13 61. Chest. 2005 Jul;128(1):203-6 81 Palliative Care of Pulmonary Emboli Main Menu… Palliative Care of Pulmonary Emboli Most deaths from PE are a result of inadequate prophylaxis Which end of life patients should receive prophylaxis? End stage cardiopulmonary patients Cancer patients with prothrombotic tumors Minimal data on prophylactic treatment VTE in end of life outpatients 83 Palliative Care of Pulmonary Emboli Current VTE Prophylaxis Hydration Not crossing legs Traditional stockings probably Encouraging mobility not effective Drug therapy Low molecular weight heparin is preferred No prothrombin time needed Once daily injection Warfarin INR should be 2-3 Difficult to regulate in the end of life patient because of other drug therapies and fluctuating liver functions 84 Palliative Care of Pulmonary Emboli On the horizon… Ximelagatran Oral medication As effective as low dose warfarin with enoxaparin Not yet approved because of potential hepatotoxicity and ↑ incidence of coronary events Idraparinux Once weekly injection In phase III trials 62. Semin Vasc Med. 2005 Aug;5(3):276-84 85 Palliative Care of Stridor Main Menu… Palliative Treatment of Stridor Causes Infection – epiglottitis, diphtheria Tumor Aspirated objects Thick sputum Blood clots Foreign bodies Dislodged tumor particles Crohn's Disease – rare – resistant to dexamethasone (54) Diffuse Idiopathic Skeletal Hyperostosis (DISH) Forestier’s Disease – from large cervical spine osteophytes compressing the trachea (55) Achalasia – megaesophagus compression of trachea (56) Myasthenia gravis – presenting with exertional stridor (57) Psychogenic stridor (58) Drug hypersensitivity – amphotericin (60) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 902 54. Chest. 2006 Aug;130(2):579-81 55. J Laryngol Otol. 1999 Jan;113(1):65-7 56. Eur J Gastroenterol Hepatol. 1997 Nov;9(11):1125-8 57. Thorax. 1996 Jan;51(1):108-9 59. Gen Hosp Psychiatry. 1994 May;16(3):213-23 60. Ann Allergy Asthma Immunol. 2003 Nov;91(5):460-6 87 Palliative Treatment of Stridor Treatment – Non-pharmacologic and Pharmacologic Treatment Postural manipulation Heimlich maneuver – for acute onset stridor Physiotherapy Bronchoscopy or laryngoscopy Tracheostomy Stents Medications Dexamethasone 16 mg po qd for edema or inflammation Oxygen / Helium 4:1 Mixture Infliximab – for Crohn’s Disease (54) 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 902 54. Chest. 2006 Aug;130(2):579-81 88 Palliative Care of Neuromuscular and Restrictive Pulmonary Disorders Main Menu… Palliative Care of Neuromuscular Disorders and Restrictive Pulmonary Disease Hypercapnia and sleep disorders are very common in neuromuscular disorders MS and ALS – bulbar disorders result in dysphagia and frequent aspiration and pneumonia Long term anticoagulation is often prescribed for thromboembolic prophylaxis Glossopharyngeal breathing is a good technique to improve ventilation in patients with high cervical injuries 90 Palliative Care of Neuromuscular Disorders and Restrictive Pulmonary Disease Non-invasive mechanical ventilation Rocking beds Abdominal pneumatic belts Negative pressure ventilators Nasal CPAP 91 Palliative Care of Bronchiectasis and Cystic Fibrosis Main Menu… Palliative Care of Bronchiectasis and Pulmonary Fibrosis Nebulized Deoxyribonuclease (DNAse) Hydrolysis of extranuclear DNA that accumulates with neutrophil degradation in infected airways Useful in cystic fibrosis and to a lesser extent in bronchiectasis 40. Derek, D. et al. (2004). Oxford Textbook of Palliative Medicine, pp. 908 93 Palliative Care of α-1 Antitrypsin Deficiency Main Menu… Palliative Care of α-1 Antitrypsin Deficiency “AAT replacement therapy is for enzyme deficient patients with impaired FEV-1 (3565% of predicted value), who have quit smoking and are on optimal medical therapy but continue to show a rapid decline in FEV-1 after a period of observation of at least 18 months.”(63) 63. Treat Respir Med. 2005;4(1):1-8 95 Happy Trails from Lea County, NM 96 Links - 1 Spiriva Cost Spiriva vs. Serevent Respiratory. 2006 Sep;11(5):598-602 Is a long-acting inhaled bronchodilator the first agent to use in stable chronic obstructive pulmonary disease? Emerging drugs for the treatment of chronic obstructive pulmonary disease. Pharmacologic treatment of chronic obstructive pulmonary disease: past, present, and future. Names of leukotriene related drugs Effect of Intravenous Magnesium Sulfate on Chronic Obstructive Pulmonary Disease Addition of anticholinergic solution prolongs bronchodilator effect of beta 2 agonists Comparison of the bronchodilating effect of salmeterol and zafirlukast in combination Retrospective evaluation of systemic corticosteroids for the management of acute exacerbations Efficacy and safety of inhaled corticosteroids in patients with COPD Roflumilast for the treatment of chronic obstructive pulmonary disease Corticosteroids and Chronic Obstructive Pulmonary Disease Theophylline in chronic obstructive pulmonary disease: new horizons. Corticosteroid resistance in chronic obstructive pulmonary disease: inactivation of histone deacetylase. Inhaled corticosteroids and mortality in chronic obstructive pulmonary disease. Inhaled corticosteroids in chronic obstructive pulmonary disease: is there a long-term benefit? Health-related quality of life in individuals with chronic obstructive pulmonary disease. Improving health-related quality of life in chronic obstructive pulmonary disease. 97 Links - 2 Diazepam in the treatment of dyspnea in the 'Pink Puffer' syndrome. The palliation of dyspnea in terminal disease More research needed An approach to dyspnea in advanced disease. Opioids are first line drugs Buspirone effect on breathlessness and exercise performance in patients with chronic obstructive pulmonary disease. Effects of buspirone on anxiety levels and exercise tolerance in patients with chronic airflow obstruction and mild anxiety. Sertraline effects on dyspnea in patients with obstructive airways disease Randomized, double blind, placebo controlled crossover trial of sustained release morphine for the management of refractory dyspnea A systematic review of the use of opioids in the management of dyspnea Disabling dyspnea in patients with advanced disease: lack of effect of nebulized morphine Roflumilast for the treatment of chronic obstructive pulmonary disease Effects of N-acetylcysteine on outcomes in chronic obstructive pulmonary disease (Bronchitis Randomized on NAC Cost-Utility Study, BRONCUS): a randomized placebo-controlled trial N-acetylcysteine reduces the risk of re-hospitalization among patients with chronic obstructive pulmonary disease Short-term effects of montelukast in stable patients with moderate to severe COPD Therapeutic responses in asthma and COPD. Bronchodilators Review of effects of PDE4 Inhibitors and LRAs Long-term montelukast therapy in moderate to severe COPD--a preliminary observation Current and future pharmacologic therapy of exacerbations in chronic obstructive pulmonary disease and asthma. Should patients with acute exacerbation of chronic bronchitis be treated with antibiotics? Advantages of the use of fluoroquinolones. 98 Links - 3 Short-term and long-term outcomes of moxifloxacin compared to standard antibiotic treatment in acute exacerbations of chronic bronchitis Moxifloxacin vs. Alternatives for Chronic Bronchitis Palliative Home Care for Advanced Lung Disease Is there a role for airway clearance techniques in chronic obstructive pulmonary disease? Nebulized hypertonic saline for cystic fibrosis Osmotic stimuli increase clearance of mucus in patients with mucociliary dysfunction Potential future therapies for the management of cough: ACCP evidence-based clinical practice guidelines Potential new cough therapies. Current and future drugs for the treatment of chronic cough Comparison of lidocaine and bronchodilator inhalation treatments for cough suppression in patients with chronic obstructive pulmonary disease. Lidocaine inhalation for cough suppression Effect of indomethacin on bronchorrhea in patients with chronic bronchitis, diffuse panbronchiolitis, or bronchiectasis In vivo study of indomethacin in bronchiectasis: effect on neutrophil function and lung secretion Stridor in Crohn disease and the use of infliximab 99 Links - 4 An unusual case of stridor due to osteophytes of the cervical spine: (Forestier's disease). Myasthenia gravis presenting with stridor Achalasia presenting as acute stridor Psychogenic stridor Amphotericin-induced stridor: a review of stridor, amphotericin preparations, and their immunoregulatory effects Use of the Dumon Y-stent in the management of malignant disease involving the carina: a retrospective review of 86 patients Thoracic embolotherapy for life-threatening hemoptysis: a pulmonologists perspective Bronchial and non bronchial systemic artery embolization for life-threatening hemoptysis: a comprehensive review Pulmonary hypertension and right heart failure in chronic obstructive pulmonary disease Advances in the treatment of secondary pulmonary hypertension Overview of treprostinil sodium for the treatment of pulmonary arterial hypertension Sildenafil for pulmonary hypertension Oral sildenafil is an effective and specific pulmonary vasodilator in patients with pulmonary arterial hypertension: comparison with inhaled nitric oxide Treatment of Pulmonary Hypertension Interferon gamma-1b as therapy for idiopathic pulmonary fibrosis. An intra-patient analysis. Interferon gamma-1b therapy for advanced idiopathic pulmonary fibrosis Interferon gamma-1b in the treatment of idiopathic pulmonary fibrosis Interferon-gamma1b therapy in idiopathic pulmonary fibrosis: a metaanalysis Emphysema in alpha1-antitrypsin deficiency: does replacement therapy affect outcome? Ximelagatran vs low-molecular-weight heparin and warfarin for the treatment of deep vein thrombosis: a randomized trial. 100 Links - 5 Is long-term low-molecular-weight heparin acceptable to palliative care patients in the treatment of cancer related venous thromboembolism? A qualitative study. Acceptability of low molecular weight heparin thromboprophylaxis for inpatients receiving palliative care: qualitative study. Treating patients with venous thromboembolism: initial strategies and long-term secondary prevention. Inhaled mannitol for the treatment of mucociliary dysfunction in patients with bronchiectasis: effect on lung function, health status and sputum. Improved sputum expectoration following a single dose of INS316 in patients with chronic bronchitis. 101