Transcript Document
Ray Peeples, MD
Case 1
50 y/o F with NF1
hx of meningioma debulking (2/10) and
cervical neurofibroma removal (7/09)
MRI studies showed an enhancing
superior cerebellar lesion growing over
time and eventually causing obstructive
hydrocephalus, the lesion was biopsied
9.10.09
12.1.09
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10.2.12
2.17.13
Pilocytic astrocytoma
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In one series of 100 NF1 patients with biopsied tumors, there were…
50 pilocytic astrocytomas (PA)
28 diffuse astrocytomas (Grades II—5%, III—15%, IV—7%)
17 low- grade astrocytomas, subtype indeterminate
2 pilomyxoid astrocytomas
1 desmoplastic infantile ganglioglioma
1 conventional ganglioglioma
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24 tumors arose in the optic pathways (14 PAs, 4 low-grade astrocytomas of
indeterminate type, 4 anaplastic astrocytomas, 1 pilomyxoid astrocytoma, and 1
ganglioglioma).
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Most tumors arising in setting of NF1 are pilocytic astrocytomas (PAs) and, unlike their
sporadic counterparts, have a distinctive predilection to involve the optic nerve,
chiasm, and hypothalamus.
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NF1-related optic gliomas are typically in young children and afflict 15% to 20% of NF1
patients.
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NF-1 related optic gliomas seem to have a more indolent behavior than their sporadic
counterparts and may even regress without treatment.
Rodriguez FJ, et al. J Neuropathol Exp Neurol . 67:240–249, 2008.
Case 2
26 y/o M with 2 yr hx of back pain and
lower extremity paresthesias
MRI showed and intradural lesion in the
L spine
MRI brain showed multiple enhancing
cerebellar lesions
Spinal lesion was resected
T2
T1
T2
T1 C+
T2
FLAIR
T2
T1 +C
Myxopapillary ependymoma, metastatic
Case 3
35 y/o M with 1 year hx of back pain and
RLE weakness
sent from outside institution with
presumptive diagnosis of L3
schwannoma with MRI performed
without contrast
EMG showed L3 and S1 radiculopathy
L3 mass was resected
T2
T1
T2
T1
L3
T1
S1
T2
Sarcoidosis
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Spinal syndromes are reported at clinical presentation in
6% to 8% of patients with neurosarcoidosis
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Spinal sarcoidosis can be intramedullary, intradural
extramedullary, epidural, or in vertebral bodies.
•
Most cases are intramedullary.
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Intradural, extramedullary spinal sarcoidosis is extremely
rare, with only 8 cases reported in the literature as of
2006.
Schaller B, et al. The Spine Journal 6:204–210, 2006.
Case 4
26 y/o M who presented in 10/2012 with
seizure
CT/MRI showed L frontal low density
lesion in white matter with no
enhancement, this lesion was biopsied
FLAIR
T1
T1
T2
T1 C+
T1 C+
Gliomatosis cerebri