Transcript OE-MM-FAQs
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The opinions expressed are those of the presenters and are not to be construed as those of the publisher or grantors. Pre-activity Survey • Please take out the Pre-activity Survey from your packet • It is important that you fill out the demographic information at the top of the form • Your answers are important to us and will be used to help shape future CME activities Polling Question Pre-activity Survey Please rate your level of confidence in your ability to treat and manage patients with multiple myeloma (MM): 1 Not at all confident 2 3 4 5 Expert Polling Question Pre-activity Survey A 55-year-old patient presents with a progressive mild decrease in hemoglobin, but is asymptomatic for MM. His workup revealed a hemoglobin of 11, calcium of 9.2, paraprotein peak of 2.6 with a beta-2 microglobulin of 3.7, and 30% plasma cells with diploid cytogenetics and no high-risk FISH. What further workup would you recommend at this time? A. No further work-up recommended B. MRI and/or PET/CT C. Gene expression profiling D. Immune spectrotyping Polling Question Pre-activity Survey Over a 4-month period, a patient receives 5 cycles of lenalidomide/dexamethasone and bortezomib and achieves a partial response. What is your treatment recommendation for this patient? A. Continue on RVD B. Change to other treatment C. Proceed to stem-cell harvest and autograft consolidation Polling Question Pre-activity Survey A patient relapses after an 18-month complete response following consolidation with melphalan, autologous stem-cell rescue, and lenalidomide daily maintenance. She is treated with 6 cycles of bortezomib/dexamethasone; however, a month later, kappa-light chains and FDG avid bone lesions on PET/CT increase. Which treatment is most suitable for this patient? A. Cyclophosphamide/bortezomib/dexamethasone B. Salvage melphalan 200 mg/m2 with autologous stem-cell rescue C. Bortezomib/lenalidomide/dexamethasone D. Carfilzomib-based combinations OR pomalidomide/low-dose dexamethasone E. Lenalidomide/dexamethasone Polling Question Pre-activity Survey Which of the following factors would NOT impact treatment selection for relapsed/refractory MM: A. Prior lines of therapy B. Myeloma genomics C. Comorbidities D. Personal lifestyle E. Clinical trial option F. None of the above, since all these factors would impact treatment selection Educational Objectives • Discuss the role of cytogenetic and molecular analyses in personalizing care in MM • Review the treatment course for patients with smoldering MM • Assess the optimal use of induction therapy and transplant to improve patient survival in MM • Evaluate the use of high-dose chemotherapy vs novel agents for relapsed/refractory MM Smoldering Multiple Myeloma FAQs Regarding Smoldering Myeloma • How do I treat a patient who presents with none of the common symptoms for myeloma (bone marrow clonal plasma cells just greater than 10, monoclonal peak barely at 3, mild anemia and no other symptoms related to the disease)? • Do I really have to wait for a patient to have a calcium level of 11, creatinine level of 2, or less than 12 grams of hemoglobin or to get infected before I initiate treatment? Case Presentation 54-year-old male 2/11 progressive mild decrease in hemoglobin. No symptoms and normal exam. W/up reveals Hb 11; Ca 9.2; IgG 3786; albumin 4.2; mpeak 2.6; B2M 3.7 BMA 30% plasma cells Diploid cytogenetic no high-risk FISH Case Question What further work-up is recommended? 1. No further work-up recommended 2. MRI and PET CT 3. Gene expression profiling 4. Immune spectrotyping Specific Diagnostic Tests • Laboratory analysis – Complete blood count and complete metabolic panel • β2M, LDH – M proteins • Radiologic imaging – Skeletal survey, MRI/CT, PET • Bone marrow biopsy • Specific tests to rule out other • Causes of anemia, renal insufficiency, • Hypercalcemia, etc. National Comprehensive Cancer Network (NCCN) Guidelines for Diagnosis of Multiple Myeloma. Differential Diagnosis Premalignant condition Plasma cell malignancy MGUS1-4 (Monoclonal Gammopathy of Undetermined Significance) Smoldering Multiple Myeloma1-5 Multiple Myeloma6-7 Asymptomatic Asymptomatic Symptomatic (~89%) Active treatment No No or clinical trial Yes M-protein (per dL) <3 g >3 g M-spike or plasmacytoma Clonal plasma cells in bone marrow <10% >10% >10% End-organ damage None None 1 or more CRAB criteria 1% per year 10% per year for first 5 years; 73% by 15 years Not Applicable Symptoms Likelihood of progression 1. Kyle RA et al. N Engl J Med. 2007;356:2582-2590. 2. International Myeloma Working Group. Br J Haematol. 2003;121:749-757. 3. Jagannath S et al. Clin Lymphoma Myeloma Leuk. 2010;10:28-43. 4. Kyle RA et al. Curr Hematol Malig Rep. 2010;5:62-69. 5. Mateos M-V et al. Blood. 2009;114:Abstract 614. 6. Durie BG Salmon SE. Cancer. 1975;36:842-854. 7. Durie BG et al. Leukemia. 2006;20:1467-1473. CRAB CRITERIA HyperCalcemia Renal dysfunction Anemia Bone lesions Increased Infections Case Presentation MRI no lesions PET CT negative Marrow 30% plasma cells diploid cytogenetics Dxd with asymptomatic myeloma What is the risk of this patient to progress to symptomatic myeloma? Risk Factors For Progression Reference Wisloff Factor % BM/PC >20 Lytic Lesions + M peak Dimop Preoteinuria >50 mg/24h Witzig >3 gm Circulating PC Hb FLC ratio FISH Low risk Int risk High risk Facon Dipenz >20 >10% >3gm >2gm (IgA) >3 gm Rajkumar Kastritis >60% + <12 >8 >100 Normal Others T4,14 or Del17 TTP 0 Risk 39 m 61 m 9m >50 m > 60 m >60 m 73 m TTP All Risk 10m 10 m 30 m 6m 24 m 24 m 8m Disease Progression in SMM and MGUS Patients Smoldering Multiple Myeloma 10% risk of progression per year* • Screen every 4-6 weeks *For first 5 years, ~3% per year for next 5 years, ~1% per year thereafter MGUS 1% risk of progression per year • First year: screen every 3 to 6 months • After first year: screen at least every 1 to 2 years • 3% of people older than 50 years • 5% of people older than 70 years Kyle RA et al. N Engl J Med. 2007;356:2582-2590. Jagannath S et al. Clin Lymphoma Myeloma Leuk. 2010;10:28-43. Kyle RA et al. Curr Hematol Malig Rep. 2010;5:62-69. Algorithm for Reclassifying SMM and Active MM *Consider including patients with the following FISH: deletion 17p, t(4;14), and 1q21 gains as active MM; this population could account for as many as 30% of SMM patients. §Consider using more than 1 fluorodeox. ARajkumar et al, 2014, Lancet Oncology, 15(12), e538-e548; Dispenzieri A et al. Blood. 2013;122:4172-4181. Proposed Guidelines on Follow-up and Management of SMM Patients suspected to have MM should first be defined as having MGUS, SMM, or myeloma requiring therapy. Ghobrial IM, Landgren O. Blood. 2014;124:3380-3388. © 2014 American Society of Hematology. Evidence for Early Treatment of High-risk SMM with Lenalidomide plus Dexamethasone Survival Outcomes in the Per-Protocol Population A B • Major Pitfalls of Mateos Study C – Control group DID NOT receive lenalidomide – Control group did not receive uniform treatment (some actually may have received MP) • Notwithstanding • Magnitude of benefit dramatic Mateos et al. N Engl J Med. 2013;369:438-447. Main Limitation of the Mateos Study “…One limitation of the study was that patients received treatment off-protocol at the time of disease progression to symptomatic myeloma. It would have been informative to examine early treatment with lenalidomide and dexamethasone versus treatment with lenalidomide and dexamethasone that was deferred until the time of progression. However, the combination of lenalidomide and dexamethasone is not an approved first-line regimen for newly diagnosed multiple myeloma, and most patients in this study (81%) were treated with either bortezomib-based regimens (53% of patients) or induction therapy followed by autologous stem-cell transplantation (28%) at the time of progression…” Summary • Asymptomatic myeloma is an entity that needs to be better defined – All patients with newly diagnosed asymptomatic myeloma need to be followed closely for the first 2-3 years (every 6-12 week visits) – All patients should be encouraged to participate in clinical trials – Patients with high-risk disease should be treated as symptomatic myeloma Case Presentation Over the next 6 months develops progressive anemia to a Hb of 10gm/dL Bone marrow now shows 60% plasma cells 15% show deletion 17 by FISH Karyotype normal No lytic lesions Is there an optimal induction regimen? FAQs for Induction • Have we fully defined the role of molecular and cytogenetic classifications in myeloma? • What is the optimal induction regimen? • How much induction treatment should a transplant-eligible patient receive? • Should I recommend SCT for a patient who has failed to achieve a PR or CR after receiving 5 cycles of induction therapy? • Is allogeneic transplant a reasonable option for a patient with standard-risk disease? Multiple Myeloma Treatment Linesa Front-line treatment Induction IMiD: Thal-Len Proteasome Inhibitor: Bor-Car Steroids: Dex-Pred Alkylator: Cyclo-Mel Anthracycline: LipoDnr-Adr Consolidation SCT Maintenance Relapsed Maintenance Rescue Observation IMiD: Thal-Len Proteasome Inh-Bor Steroids: Dex-Pred IMiD: Thal-Len-Pom Proteasome Inh: Bor-Car Steroids: Dex-Pred Alkylators: Mel-Cy-Benda Investigational aTransplant-eligible patients. Bor/Dex = bortezomib, dexamethasone; Bor/Dex/Dox = bortezomib, dexamethasone, doxorubicin; Bor/Thal/Dex = bortezomib, thalidomide, dexamethasone; Len/Dex = lenalidomide, dexamethasone; SCT = stem-cell transplant; Thal/pred = thalidomide, prednisone; Bor/Liposomal/Dox = bortezomib, liposomal doxorubicin. NCCN, 2009. Impact of Chromosomal Abnormalities on Survival Outcomes in MM (cont.) IMWG Analysis Genetic Abnormalities 4-year Estimated OS Minus vs Plus Abnormality Log Rank P Value Any 73% vs 57% <0.0001 t(4;14) ISSI ISS2 ISS3 64% vs 36% 81% vs 52% 63% vs 30% 44% vs 22% <0.0001 <0.0001 <0.0001 <0.007 Del(17) ISSI ISS2 ISS3 68% vs 44% 81% vs 64% 68% vs 42% 48% vs 28% <0.0001 <0.020 <0.0001 <0.020 a. ISSI or ISS2, normal FISH 193/610 deaths (76%) b. ISSI + abnormal FISH/ISS3 + normal FISH 140/252 deaths (52%) c. ISS2 or ISS3 + abnormal FISH 146/196 deaths (32%) ISS = International Staging System Avet-Loisseau H et al. J Clin Oncol. 2009;27:4585-4590. a vs b <0.0001 a vs c <0.0001 b vs c <0.0001 Goals of Therapy Longest life with best quality of life with minimal burden of treatment A Meta-analysis of Phase III Studies Comparing Bortezomib-based vs Non-bortezomib-based Induction Treatment Before ASCT A B 100 100 80 80 Overall Survival (%) Progression-Free Survival (%) Bortezomib based Bortezomib based 60 40 Non-bortezomib based 40 20 20 Non-bortezomib based Bortezomib based No. at risk Non-bortezomib based Bortezomib based Non-bortezomib based 60 0 6 785 787 671 722 Non-bortezomib based Bortezomib based P=0.0001 0 12 18 24 30 36 42 48 54 60 Time (months) 604 675 527 609 429 491 306 360 178 212 98 101 54 58 25 31 10 10 Michele Cavo, MD. Presented at: ASH2013, Abstract #767. No. at risk Non-bortezomib based Bortezomib based 6 P=0.0402 12 18 24 30 36 42 48 54 60 Time (months) 785 787 727 746 694 722 662 698 614 641 486 515 309 338 174 191 100 117 52 60 Sonneveld P. J Clin Oncol. 2013;31:3279-3287. 18 20 Case Presentation Over the next 3 months receives 4 cycles of lenalidomide / dexamethasone and bortezomib and achieves a PR Stem cells are collected Case Question What would you recommend for this patient? • Continue on RVD? • Change to other treatment? • Proceed to autograft consolidation? Autologous Bone Marrow Transplant – Long-term Results Barlogie B et al. Bone Marrow Transplant. 1998;21:1101-1107. Role of High-dose Melphalan in Myeloma in the Era of IMiDs and Proteasome Inhibitors Benefit of Autografting for Myeloma Figure 2 Koreth J et al. Biol Blood Marrow Transplant. 2007;13:183-196. (DOI:10.1016/j.bbmt.2006.09.010). Copyright © 2007 American Society for Blood and Marrow Transplantation. Terms and Conditions. IFM/DFCI 2009 Study Newly Diagnosed MM Patients (SCT Candidates) Randomize, stratification ISS & FISH VRD x 3 CY (3g/m2) MOBILIZATION Induction VRD x 3 Collection CY (3g/m2) MOBILIZATION Goal: 5 x106 cells/kg Goal: 5 x106 cells/kg Melphalan 200mg/m2* + ASCT VRD x 5 Consolidation Lenalidomide 12 mos VRD x 2 Lenalidomide 12 mos Maintenance http://www.clinicaltrials.gov/ct2/show/NCT01208662?term=nct01208662&rank=1. SCT at relapse MEL 200 mg/m2 if <65 yrs, ≥65 yrs 140mg/m2 Mel200-ASCT vs CC+R: PFS1 Median Follow-up from Randomization: 4 Years Gay et al, Blood, 2014 124(21). Abstract 198. Mel200-ASCT vs CC+R: Second-line Therapy Gay et al, Blood, 2014 124(21). Abstract 198. Mel200-ASCT vs CC+R: OS Median Follow-up from Randomization: 4 Years Gay et al, Blood, 2014 124(21). Abstract 198. Mel200-ASCT vs CC+R Mel200-ASCT vs CC+R OS Subgroup analysis HR (95% CI) P value Age <60 0.67 (0.41-1.11) 0.117 Age ≥60 0.44 (0.23-0.86) 0.015 KPS 60-70% 0.76 (0.33-1.72) 0.506 KPS 80-100% 0.54 (0.34-0.85) 0.008 ISS I/II 0.55 (0.34-0.89) 0.016 ISS III 0.75 (0.38-1.45) 0.376 No del17, t(4;14), t(14;16) 0.57 (0.34-0.94) 0.029 Del17, t(4;14), t(14,16) 0.60 (0.31-1.14) 0.118 LDH < ULN 0.62 (0.41-0.95) 0.027 LDH ≥ ULN 0.23 (0.03-1.92) 0.177 Favors Mel200-ASCT Favors CC+R OS, overall survival; KPS, Karnofsky Performance Status; ISS, International Staging System; LDH, lactate dehydrogenase; ULN, upper limit of normal; Mel200-ASCT, melphalan 200 mg/m2 followed by autologous stem cell transplantation; CC+R, conventional chemotherapy + lenalidomide Gay et al, Blood, 2014 124(21). Abstract 198. 1st Autologous Transplant n=710 No Sibling Donor Auto-Auto n=484 High Risk n=48 Sibling Donor Auto-Allo n=226 Standard Risk Standard Risk n=436 n=189 Main groups compared High Risk n=37 Survival Outcomes after the First Transplant Auto-Auto vs Auto-Allo: Intent-to-treat analysis Progression-free Survival 100 Overall Survival Auto/Auto, 80% @ 3yr Auto/Auto, 46% @ 3yr 90 100 90 80 80 Probability, % 70 70 Auto/Allo, 77% @ 3yr 60 60 50 50 Auto/Allo, 43% @ 3yr 40 40 30 30 20 20 10 10 P-value = 0.67 0 Months # at risk: 0 Auto/Auto 436 Auto/Allo 189 P-value = 0.19 0 6 12 18 24 30 36 42 48 0 6 12 18 24 30 36 42 48 395 165 348 138 292 117 242 105 213 89 178 71 54 42 23 16 436 189 424 183 406 167 395 160 370 156 348 143 305 124 107 43 79 27 CALGB 100104 Schema Registration D-S Stage 1-3, ≤70 years ≥2 cycles of induction Attained SD or better ≤1 yr from start of therapy ≥2 x 106 CD34 cells/kg Restaging Days 90–100 Randomization Placebo Mel 200 ASCT CR PR SD Stratification based on registration -2M level and prior thalidomide and lenalidomide use during Induction. Primary Endpoint: powered to determine a prolongation of TTP from 24 months to 33.6 months (9.6 months) Lenalidomide* 10 mg/d with ↑↓ (5–15 mg) * provided by Celgene Corp, Summit, NJ Time to Progression CALGB 100104; N Engl J Med. 2012. Multivariate Analysis of Prognostic Factors for PFS Variable PFS HR 95% CI P < CR at induction 1.80 1.29-2.51 0.001 Del(17p) and/or t(4;14) 1.56 1.18-2.05 0.002 ISS > 2 1.57 1.14-2.17 0.006 Plts <150 (109/L) 1.48 1.05-2.08 0.025 Hb <10.5 (g/dL) 1.32 1.03-1.70 0.028 Del(13q) 1.20 0.94-1.54 0.145 IgA isotype 1.13 0.85-1.50 0.393 Creat >1.2 (mg/dL) 0.87 0.64-1.19 0.391 Hazard Ratio Michele Cavo, MD. Presented at: ASH2013, Abstract #767. 1 2 PFS According to Preplanned ASCT(s) for Patients with del(17p) and/or t(4;14) and Who Failed CR after B-based Induction Regimens Score 2 ISS Prognostic factors Cytogenetic abnormalities Response at induction 1-2 Del(17p) ± t(4;14) < CR 70 (11.55%) 3 3 Del(17p) – t(4;14)Del(17p) ± t(4;14) < CR CR 65 (10.73%) 6 (0.99%) N° of pts (%) 141 (23.27%) Kaplan-Meier survival estimates 1.00 0.75 1 ASCT 0.50 2 ASCT 42 mo 21 mo 0.25 Log rank test: P=0.004 0.00 0 HR 0.41 (0.22 - 0.77) P=0.006 12 Michele Cavo, MD. Presented at: ASH2013, Abstract #767. 24 Months 36 48 OS According to Preplanned ASCT(s) for Pts With del(17p) and/or t(4;14) and Who Failed CR After B-based Induction Regimens Score 2 ISS Prognostic factors Cytogenetic abnormalities Response at induction 1-2 Del(17p) ± t(4;14) < CR 70 (11.55%) 3 3 Del(17p) – t(4;14)Del(17p) ± t(4;14) < CR CR 65 (10.73%) 6 (0.99%) N° of pts (%) 141 (23.27%) Kaplan-Meier survival estimates 1.00 0.75 2 ASCT 76% 0.50 0.25 Log rank test: P=0.0001 0.00 0 1 ASCT HR 0.22 (0.10 - 0.50) P<0.001 12 Michele Cavo, MD. Presented at: ASH2013, Abstract #767. 33% 24 Months 36 48 BMT CTN 0702: SCHEMA Lenalidomide* Maintenance Register and Randomize MEL 200mg/m2 * Bortezomib 1.3mg /m2 days 1, 4, 8,11 Lenalidomide 15mg days 1-15 Dexamethasone 40mg days 1, 8, 15 **Lenalidomide 15 mg daily x 3years VRD x 4* Lenalidomide Maintenance** MEL 200mg/m2 Lenalidomide Maintenance** Relapsed/Refractory Multiple Myeloma FAQs Regarding Relapsed/Refractory Multiple Myeloma • Is there a role for high-dose chemotherapy consolidation in the era of novel, more effective agents and strategies? Do we know the optimal timing for HD chemotherapy? • What are the pros and cons of emerging therapies and novel treatment strategies based on recent clinical data? Case Presentation • 54-year-old male with progressive anemia to Hb of 10gm/dL; Ca 9.2; IgG 6800; albumin 4.2; mpeak 4.5; B2M 5.5. No lytic lesions, but bone marrow 60% plasma cells, normal karyotype with 15% deletion 17 by FISH • Receives 4 cycles of lenalidomide/dexamethasone and bortezomib and achieves a PR, followed by consolidation with melphalan 200 mg/m2 with autologous stem cell rescue and len 10 mg po daily maintenance (along with monthly zoledronic acid) with a CR for 1.5 years and then relapses by free light chains with a kappa of 150 mg/L and KLR of 162 Case Presentation • Treated with bortezomib/dexamethasone for 6 cycles with a PR and then was off therapy for a preplanned trip. The kappa light chains increased again 35 days later to 205 and a KLR of 232 along with asymptomatic but new FDG avid bone lesions on PET-CT. Case Question Which treatment would you choose for this patient at this time? 1. Cyclophosphamide/bortezomib/dexamethasone 2. Salvage melphalan 200 mg/m2 with autologous stem cell rescue 3. Bortezomib/lenalidomide/dexamethasone 4. Carfilzomib-based combinations 5. Pomalidomide/low-dose dexamethasone 6. Lenalidomide/dexamethasone 7. Unsure Factors to Consider in Treatment Selection • CRAB symptoms, disease burden, and rate of progression • Prior therapies – Depth and duration of prior response – Side effects – Time since therapy • Myeloma genomics • General health – diabetes, CBC, cardiac/hepatic/renal function, neuropathy, VTE • Personal lifestyle and preferences • Option for clinical trial MM-003 Final Analysis: Pomalidomide/LoDex vs HiDex in Relapsed/Refractory MM: Efficacy Data PFS* 1.0 Median PFS, Mos 0.8 Pom + LoDex (n = 302) 4.0 HiDex† (n = 153) 1.9 Proportion of Patients Proportion of Patients 1.0 OS 0.6 HR: 0.50 P <0.001 0.4 0.2 0 Median OS, Mos 0.8 4 8 12 16 20 24 13.1 HiDex† (n = 153) 8.1 0.6 0.4 0.2 HR: 0.72 P =0.009 0 0 Pom + LoDex (n = 302) 0 4 PFS (Mos) 8 12 16 OS (Mos) • ORR (overall): 31% (26% PR) Pom/LoDex vs 10% (9% PR) HiDex *Primary endpoint. †85 pts (56%) on the HiDex arm received subsequent Pom. San Miguel J et al. Lancet Oncol. 2013;14:1055-1066. Dimopoulos MA et al. Presented at: ASH 2013, Abstract #408. Reproduced with permission. 20 24 28 Pomalidomide/LoDex vs HiDex: Safety • AEs generally similar between arms and across subgroups – Most common grade 3/4 AEs: neutropenia, anemia, thrombocytopenia – ≥ grade 3 PN in 15% with Pom plus LoDex vs 11% with HiDex Pom + LoDex (n = 300) AE, % HiDex (n = 150) Grade 3 Grade 4 Grade 5 Grade 3 Grade 4 Grade 5 Infections and infestations 24 6 4 19 5 9 Anemia 31 2 -- 32 5 -- Neutropenia 26 22 -- 9 7 -- Fatigue 5 -- -- 6 -- -- Thrombocytopenia 9 13 -- 9 17 -- Pyrexia 3 <1 -- 3 1 -- Diarrhea 1 -- -- 1 -- -- Constipation 2 -- -- -- -- -- <1 <1 -- <1 -- -- Back pain 4 1 -- 3 <1 -- Dyspnea 4 1 -- 5 -- -- Febrile neutropenia 8 2 -- -- -- -- Cough San Miguel J et al. Lancet Oncol. 2013;14:1055-1066. Carfilzomib, an Irreversible Proteasome Inhibitor, in Relapsed/Refractory MM – Approval based on single-arm phase II PX-171-003 study (n = 266): ORR of 23.7% and median DOR of 7.8 mos[1] Pts Alive and Without Progression (%) • Carfilzomib FDA approved in 2012 for treatment of MM after ≥2 previous therapies, including bortezomib and an IMiD, and with progression on or within 60 days of treatment PFS 100 Median PFS: 3.7 mos (95% Cl: 2.8-4.6) 75 50 25 Censored observations Confidence band 0 0 1. Siegel DS et al. Blood. 2012;120:2817-2825. 2. NCCN. Clinical practice guidelines in oncology: multiple myeloma. v.1.2014. 2.5 5.0 7.5 10.0 12.5 15.0 Mos From Start of Treatment 17.5 Integrated Safety Profile of Single-agent Carfilzomib: Experience from 526 Patients • 4 phase II studies (PX-171-003-A0, PX-171-003-A1, PX-171-004, and PX-171-005) Select AEs, % All Grades Related Grade 3/4 Serious AE Fatigue Anemia Nausea Any cardiac event Cardiac failure Any respiratory event Dyspnea Any renal impairment Serum creatinine Acute renal failure 55.5 46.8 44.9 22.1 7.2 69.0 42.2 33.1 24.1 5.3 41.4 26.8 35.2 NR 7.6 22.4 1.3 9.5 5.7 10.3 4.9 7.2 2.7 4.4 0 1.3 0 7.8 4.9 6.5 2.1 6.1 1.3 4.2 Peripheral neuropathy 13.9 NR 1.3 NR NR NR • Tolerable safety profile allows for administration of full-dose carfilzomib with low discontinuation rates Siegel D et al. Hematologica. 2013;98:1753-1761. Single Agent and Doublet Efficacy ORR PFS (months) OS (months) 0% 30% 2y : 20% 2y : 48% 49% 0% 38% 6.22 30 646 41% 0% 43% 9 33 3 177 41% 10% 61% 11.1 29.6 Len Dex MM010 3 349 30% 4.5% 60% 11.3 38 CFZ (+dex 8) 2 266 100% 99% 23.7% 3.7 15.6 Pom D vs Dex 3 302 100% 95% 31% 4.2 13.1 Trial IMiD PI exposed exposed Phase n Thalidomide 2 169 0% BTZ vs DEX 3 669 BTZ + doxil vs BTZ 3 Len Dex MM009 Barlogie B. Blood. 2001;98:492-494. Richardson P. N Engl J Med. 2005;352:2487-2498. Orlowski RZ. J Clin Oncol. 2007;25:3892-3901. Weber D. N Engl J Med. 2007;357:2133-2142. Dimopoulos M. N Engl J Med. 2007;357:2123-2132. Siegel DS. Blood. 2012;120:2817-2825. San Miguel J. Lancet Oncol. 2013;14:1055-1066. Phase III CarRd vs Rd (ASPIRE) Study Design 28-day cycles CarRd Key inclusion criteria: • 1–3 prior treatments • Relapsed or PD • ≥PR to at least 1 prior regimen Key exclusion criteria: Carfilzomib 27 mg/m2 IV (10 min) Days 1, 2, 8, 9, 15, 16 (20 mg/m2 days 1, 2, cycle 1 only) Lenalidomide 25 mg Days 1–21 Dexamethasone 40 mg Days 1, 8, 15, 22 Randomization n=792 After C12, carfilzomib given D 1, 2, 15, 16 After C18, carfilzomib discontinued • CrCl <50 mL/min • PD on BTZ • PD on Rd • Len or dex intolerance Rd Lenalidomide 25 mg Days 1–21 Dexamethasone 40 mg Days 1, 8, 15, 22 Primary Endpoint: Progression-free Survival ITT Population (n=792) Primary Endpoint: Progression-free Survival by Subgroup 23.1 vs 13.9 mos (P 0.083) 29.6 vs 19.5 mos (P 0.004) Kaplan-Meier 24-Month Overall Survival Rates Percentage of Patients 80 70 60 CarRd 50 40 30 73.3% Rd 65.0% 20 10 0 • Unadjusted P value from the stratified log-rank test comparing the overall survival curves up to 24 months was 0.0046 Adverse Events in the Safety Population Stewart AK et al. N Engl J Med. 2014. DOI: 10.1056/NEJMoa1411321. PI + IMiD + Dex (Triplet) Efficacy Trial Phase n IMiD exposed IMiD PI PI refractory exposed refractory ORR PFS OS (mos) (mos) Bort Thal Dex 1-2 85 74% most 0% 0% 65% 6 22 Bort Len Dex 2 64 73%T 6% L 3% 53% 8% 64% 9.5 30 Bort Pom Dex 1 28 100% 100% 100% NA 71% NA NA Car-LenDex 2 52 73% 44% 80% 25% 77% 15.4 NA Car-PomDex 1/2 79 100% 100% 89% 91% in ph 1 Pineda-Roman M. Leukemia. 2008;22:1419-1427. Richardson PG et al. Blood. 2014;123:1461-1469. Richardson PG et al. Presented at: ASCO 2014. 70% Wang M et al. Blood. 2013;122:3122-3128. Shah JJ et al. Presented at: ASH 2013. Abstract 690. 9.7 NR PANORAMA 1: Phase III Study of Panobinostat + Bortezomib + Dexamethasone in Relapsed or Relapsed and Refractory MM Panobinostat significantly extended progression-free survival PBD n = 387 Pbo-BD n = 381 P Median PFS, mo 11.99 8.08 <0.0001 Median OS, mo 33.64 30.39 0.26 ORR, % 60.7 54.6 0.09 CR/nCR, % 27.6 15.7 0.00006 Median DOR, mo (range) 13.14 (11.76-14.92) 10.87 (9.23-11.76) Median TTR, mo (range) 1.51 (1.41-1.64) 2.00 (1.61-2.79) Panobinostat, bortezomib, and dexamethasone Placebo, bortezomib, and dexamethasone Progression-free survival (%) HR 0.63, 95% CI 0.52-0.76; P<0.0001 Time (months) • Median PFS was significantly longer in the panobinostat group • There is also a trend toward better OS in the panobinostat group • ORRs were similar for the two groups; however, the CR/nCR rate was significantly higher for panobinostat • Common grade 3-4 laboratory abnormalities and adverse events included thrombocytopenia (67% vs 31%), lymphopenia (53% vs 40%), diarrhea (26% vs 8%), asthenia or fatigue (24% vs 12%), and peripheral neuropathy (18% vs 15%) San-Miguel JF et al. Lancet Oncol. 2014;15:1195-1206. Pan + Btz + Dex Relapsed or Refractory MM Efficacy in Patients with High-risk Cytogenetics Hazard Ratio (95% CI) Overall (n=768) Cytogenetic risk group - Normal risk (n=167) - Poor risk (n=37) 0.63 (0.52-0.76) 0.88 (0.60-1.29) 0.47 (0.18-1.25) 0.25 0.5 PAN-BTZ-Dex San-Miguel JF et al. Lancet Oncol. 2014;15:1195-1206. 0.75 1 1.25 1.5 1.75 2 2.25 Pbo-BTZ-Dex Summary of Combo Therapy with HDACIs Regimen Panobinostat or placebo + VD Phase (N) III (768) Outcomes ORR: 60.7% vs 54.6% PFS: 12.0 vs 8.1 mos (P <0.0001) (9.9 vs 7.7) OS: 33.6 vs 30.4 mos Panobinostat + VD II (55 BTZ ref) Panobinostat + RD II (19) ORR of 31%, CBR of 52 % n=14 Len Ref: ORR 21%, CBR 42% Panobinostat + Carfilzomib I/II (26) ORR of 46%, CBR of 52 % n=16 Btz Ref: ORR 44% Vorinostat or placebo + V (no dex) III (637) ORR: 54% vs 41% (P <0.0001) PFS: 7.6 vs 6.8 mos (P <0.01); OS no diff Ricolinostat ± VD I (20) ORR: 25% (heavily pretreated); CBR: 60% Ricolinostat + RD I (22) ORR: 64%, CBR: 100% San-Miguel JF et al. Lancet Oncol. 2014;15:1195-1206. Richardson PG et al. Blood. 2013;122:2331-2337. Chari A. Presented at: ASH 2014. Kaufman. Presented at: ASH Abstract #32. ORR 34.5%, CBR 52.7% Dimopoulos M et al. Lancet Oncol. 2013;14:1129-1140. Raje N et al. Presented at: ASH 2013. Abstract #759. Raje N et al. Presented at: EHA 2014. Abstract #P358. CD38 Monoclonal Antibodies • CD38 - transmembrane glycoprotein & ectoenzyme with high-receptor density on MM cells1 (80%-100%) vs NHL2,3 (30%-80%) vs AML4 58% vs B-CLL5 20%-25% • Also expressed on precursor B-cells • Daratumumab and SAR650984 : humanized IgG1 monoclonal antibodies 1. Lin et al. Am J Clin Pathol. 2004;121:482-488. 2. Angelopoulou et al. Eur J Haematol. 2002;68:12-21. 3. Schwonzen et al. Brit J Haematol. 1993;83:232-239. 4. Keyhani et al. Leukemia Res. 1999;24:153-159. 5. Domingo-Domènech et al. Haematologica. 2002;87:1021-1027. Daratumumab • Part 1 (n=32): phase I, first in human – Main toxicity grade 1 or 2 infusional toxicity – 5 of 12 (42%) of patients dosed at 4-24 mg/mg achieved PR as best response • Part 2 (n= 50): expansion cohort Patient Characteristics All AEs Grade 3/4 and SAEs per Dose Group Infusion Related Reactions (IRR) Response Daratumumab Status • Breakthrough designation by FDA: May 2013 for >3 lines of therapy or PI and IMiD refractory • Newly Diagnosed – Phase III (SCT eligible): DVTD vs VTD – Phase III (non-SCT eligible): DRd vs Rd – Phase III (non-SCT eligible): DVMP vs VMP • Relapse (1+ lines of therapy) – Phase III: DRd vs Rd – Phase III: DVD vs VD • Relapsed/Refractory – Phase II: Dara – Phase II: Dara + [VD, VMP, VTD, PomD] Indatuximab Ravtansine (BT062): Antibodydrug Conjugate vs CD138 • An anti-CD138 chimerized monoclonal IgG4, covalently linked to the cytotoxic agent maytansinoid (DM4) • CD138 is highly expressed on MM cells but not other hematopoietic and marrow stromal cell • To a lesser extent CD138 can also be found on epithelial cells • BT062 is stable and non-toxic in circulation 1. Binding to CD138 2. Receptor (CD138)-mediated internalization 3. Lysosomal processing of SPDB linker leads to lipophilic DM4 metabolites (DM4 + S-methyl-DM4) 4. Inhibition of tubulin polymerization 5. Cell cycle arrest and apoptosis 6. Bystander killing of neighboring cells Jagannath et al. Abstract #305. Best Response in Study 969 Number of patients Total Percentage treated with BT062 32 evaluable for response 28 100% - PD 14 50% - SD 11 39% - Minor response 2 7% - Partial response 1 4% Objective Clinical Stable Response Benefit Disease *Stabilized for at least 11 weeks (C4D15) Rate Response or better 50% 4% 11% • Median # cycles for patients with ≥SD: 5 (105 days), range 4-25 • Patient with MR ongoing, progression free >18 months • Related SAEs and DLTs in highest dose levels and CD138+ tissues; resolved after 10-52 days - DLTs: elevated ggt, mucositis, HFS - SAE: as above + GIB, blurred vision/dry eyes/photophobia due to corneal epithelial damage, acneiform rash Jagannath et al. Abstract #305. Summary of Efficacy of Monoclonal Antibodies (@ R2P2/Ph3 Doses) Treatment n Eligibility (% Refractory) Response Rate PFS DOR (mos) OS (mos) Elotuzumab Rd 36 NA -R sens 92% 33 mos 17.8 NR Daratumumab 20 50/75/38 (% Ref: B/L/BL 35% (n=20) NR NR NR Sar650984 13 69% C&P exposed 30.8% NA 5+ NA Dara RD 30 6.7% L ref 87% NA NA NS Sar RD 24 80%L/20%P ~60 B/~50%Car (48% L ref, n25) 63% 5.8 mos NA NA BT062 RD 21 100%Bort, 87%L 73% NA NA NA (75% L ref, n8) Dara Breakthrough designation May 2013 for >3 lines of therapy or PI and IMiD refractory Elo Breakthrough designation by FDA: May 19 2014 for >1 line of therapy given with Rd 1. Lonial S et al. ASCO 2013. Abstract 8542. 3. Martin T et al. ASCO 2014. Abstract 8532. 5. Martin T et al. ASH 2014. Abstract 83. 2. Lokhorst HM et al. ASCO 2014. Abstract 8513. 4. Plesner T et al. ASH 2014. Abstract 84. 6. Kelly K et al. ASH 2013. Abstract 758. Kinesin Spindle Protein – A New Drug Target in Multiple Myeloma (MM) • Kinesin Spindle Protein (KSP, eg5) is a microtubule motor protein required for mitosis and separation of spindle pole – KSP inhibition prevents formation of bipolar spindle, leading to cell death • Rapid onset of apoptosis occurs in Mcl-1 Dependent MM • Expected Differentiated AE profile – No expected neuropathy – Minimal non-hematological toxicity Tunquist BJ et al. Mol Cancer Ther. 2010;9:2046-2056. Hematologic Toxicity Worst Grade On-Study Filanesib Single-agent Filanesib + Dex N=55 N=32 Neutrophils Platelets Hemoglobin Bleeding Febrile Neutropenia 0 25 50 75 100 0 25 Grade 3 Grade 4 Hematological toxicity predicted based on mechanism of action • Managed with supportive care • Low incidence of febrile neutropenia or bleeding events 50 75 100 Filanesib Activity Filanesib granted orphan drug approval by FDA in May 2014. Summary of Novel Agents with Single-agent Activity Treatment n Eligibility ixazomib + dex 33 filanesib in low AAG filanesib + dex in low AAG ORR PFS DOR OS (mos) (mos) 88% Lexp; B sens 34% 12.4 32 21 75% IMiD Ref 53% PI ref 16% 24% 3.7 5.3 8.6 8.6 55 36 100% IMiD Ref 98% PI ref 15% 19% 3.4 5.1 5.1 5.1 10.5 10.8 afuresertib 34 97% I; 88% PI 8.8% selinexor + dex 8 Ref to all classes 50% NR NR NR LGH 447 59 NR 10.5% NR 5.8 NR Filanesib granted orphan drug approval by FDA in May 2014. Kumar S et al. ASH 2013. Lonial S. ASH 2013. Voorhees et al. ASH 2013. Chen C et al. EHA 2014. Spencer A et al. Blood. 2014. Raab et al. ASH 2014. Abstract 301. 96% @ 6 mo 19 23.3 Participant CME Evaluation • Please take out the Participant CME Post-survey and Evaluation Form from the back of your packet. • If you are not seeking credit, we ask that you fill out the information pertaining to your degree and specialty, as well as the few post-activity survey questions measuring the knowledge and competence you have garnered from this program. The post-survey begins on page 1 of the evaluation form. • Your participation will help shape future CME activities. Polling Question Post-activity Survey A 55-year-old patient presents with a progressive mild decrease in hemoglobin, but is asymptomatic for MM. His workup revealed a hemoglobin of 11, calcium of 9.2, paraprotein peak of 2.6 with a beta-2 microglobulin of 3.7, and 30% plasma cells with diploid cytogenetics and no high-risk FISH. What further workup would you recommend at this time? A. No further work-up recommended B. MRI and/or PET/CT C. Gene expression profiling D. Immune spectrotyping Polling Question Post-activity Survey Over a 4-month period, a patient receives 5 cycles of lenalidomide/dexamethasone and bortezomib and achieves a partial response. What is your treatment recommendation for this patient? A. Continue on RVD B. Change to other treatment C. Proceed to stem-cell harvest and autograft consolidation Polling Question Post-activity Survey A patient relapses after an 18-month complete response following consolidation with melphalan, autologous stem-cell rescue, and lenalidomide daily maintenance. She is treated with 6 cycles of bortezomib/dexamethasone; however, a month later, kappa-light chains and FDG avid bone lesions on PET/CT increase. Which treatment is most suitable for this patient? A. Cyclophosphamide/bortezomib/dexamethasone B. Salvage melphalan 200 mg/m2 with autologous stem-cell rescue C. Bortezomib/lenalidomide/dexamethasone D. Carfilzomib-based combinations OR pomalidomide/low-dose dexamethasone E. Lenalidomide/dexamethasone Polling Question Post-activity Survey Which of the following factors would NOT impact treatment selection for relapsed/refractory MM: A. Prior lines of therapy B. Myeloma genomics C. Comorbidities D. Personal lifestyle E. Clinical trial option F. None of the above, since all these factors would impact treatment selection Thank you for joining us today!