Children`s Mercy Hospital

Download Report

Transcript Children`s Mercy Hospital

Cleft Palate &/or Velopharyngeal Inadequacy Assessment or How to Determine Nose vs. Mouth Sounds

KSHA Conference Presentation 10/01/2010

Sally Helton, MS, CCC-SLP Speech/Language Pathologist

Children’s Mercy Hospitals & Clinics Kansas City, Missouri Hearing & Speech Department 913-696-5756

Introduction

• Educational Background • # Years at CMHC • # Years CMHC Cleft Palate/Craniofacial Team • # Years CMHC FFVN Team • # Years Member ACPA • Primary Job Function • Other Job Functions

Intent of Presentation

• To provide information regarding diagnostic assessment for communication disorders due to cleft lip &/or palate &/or velopharyngeal inadequacy • To provide information regarding other issues that impact cleft lip &/or palate &/or velopharyngeal inadequacy • To provide information regarding importance of team approach to treatment • To provide referral criteria for more advanced assessment, perceptual &/or instrumental

Basic Terminology

Cleft Lip

• A cleft of the lip which may be: -complete or incomplete -unilateral or bilateral -extend to the nostril -extend to the alveolus

Cleft Palate

• A cleft of the palate which may be: -complete or incomplete -unilateral or bilateral

-submucous

Cleft Palate cont’d.

-overt: observe one or more of: -bifid uvula -zona pellucida -muscular diastasis -notch in posterior border of hard palate

Cleft Palate cont’d.

• Submucous cont’d.

-occult (hidden)

Cleft Palate cont’d.

• Variations • Incidence • Other Clefts • Classification Systems

ACPA

• American Cleft Palate-Craniofacial Association

22q deletion

• Deletion of genetic material from chromosome 22 • Other names: 22q11.2 deletion Shprintzen’s Syndrome Velo-Cardio-Facial Syndrome

22q deletion cont’d.

• Other manifestations • Organ systems affects • Variable expression • Incidence • Significance in regard to education

Flexible Fiberoptic Video Nasopharyngoscopy (FFVN)

• Invasive procedure used to evaluate the structure & function of the velopharyngeal mechanism during speech.

Velopharyngeal Mechanism

• Velo: velum/soft palate • Pharyngeal: lateral & posterior pharyngeal walls • Pharynx: part of throat between esophagus & nasal cavity

Velopharyngeal Port

• Port or gateway formed by action of the pharynx & velum to control the flow of air and sound through the mouth & nasal passages

Velopharyngeal Valve

• Valve which closes & opens velopharyngeal port between nasopharynx & oropharynx • Formed by velum & aided by posterior & lateral pharyngeal walls • Nasopharynx: part of pharynx above soft palate & just behind nasal cavity • Oropharynx: part of pharynx below soft palate at the level of the oral cavity

Velopharyngeal Valve

Velopharyngeal Closure

• Closing of nasal cavity from the oral cavity • Accomplished by using velum & pharynx & possibly adenoid tissue • Directs airflow through mouth instead of the nose

Velopharyngeal Valve

Velopharyngeal Inadequacy (VPI/A)

• Generic term • Refers to any abnormal velopharyngeal function • Diagnosed perceptually (by listening)

Velopharyngeal Inadequacy cont’d.

• 3 basic subtypes: -velopharyngeal insufficiency (VPI/S) -velopharyngeal incompetency (VPI/C) -velopharyngeal mislearning Subtypes CANNOT be distinguished perceptually.

Subtypes are not mutually exclusive.

Velopharyngeal Insufficiency (VPI/S)

• Structural defect of the palate &/or pharyngeal area

Velopharyngeal Incompetency (VPI/C)

• Neurogenic impairment • Movement disorder/motor planning • Not structural

Velopharyngeal Mislearning

• Functional disorder • Faulty learning of articulation patterns • Sound (phone) specific nasal air emission (s)

Relationship of VPI/A Types

Learning (articulation disorder) VP Mislearning Anatomy (structure) VP Insufficiency (VPI/S) Physiology (movement) VP Incompetency VPI/C

Relationship of VPI/A Types cont’d.

• Significance of relationship: if types are not mutually exclusive, treatment will need to target all types presented by the patient

Relationship of VPI/A Types cont’d.

• Significance of relationship: diagnostic assessment needs to determine types of VPI/A the patient presents diagnostic assessment should include perceptual evaluation & possible instrumental/more invasive evaluation such as FFVN

Relationship of VPI/A Types cont’d.

• Instrumental diagnostic assessment with FFVN needs to be a VALID study • Use or attempted use of high pressure consonants is REQUIRED for a VALID FFVN study • If high pressure consonants are not being used/attempted, speech therapy should occur first.

Areas of Assessment

• History • Articulation • Resonance • Nasal Air Emissions (NAE) • Velopharyngeal Adequacy • Language • Voice • Fluency • Oral Mechanism/Oral Peripheral Examination

Tools Needed for Assessment

• Tissues • Gloves • Flashlight • Mirror • Reinforcers/Toys • Articulation test & score form • Language test & score form • Resonance/NAE protocol form (stimuli) • Tape recorder (optional)

Tools Needed for Assessment cont’d.

• CMHC Protocol • ACPA Universal Parameters for Assessment (The Cleft Palate-Craniofacial Journal, January 2008, Volume 45, Number 1, Henningsson et.al., pg. 1-17)

Assessment-History Areas to Consider

• Cleft: type & surgical &/or prosthetic management of • School History (including learning issues) • Medical • Speech Therapy • Psychological Issues • Feeding/swallowing • Parents’ Concerns/Perspective • Peer Interactions

Assessment-History Type of Cleft/Surgeries/Prosthesis

Type of Cleft:

- note type of cleft (i.e., left cleft lip & palate) •

Surgeries Related to Cleft/VPI/A:

- note surgeries regarding primary repair of cleft - note secondary surgeries in regard to VPI/A - note surgeries that may negatively impact VPA (i.e., tonsillectomy &/or adenoidectomy/T&A) •

Prosthetic Management of Cleft/VPI:

- note any prosthesis used in regard to cleft/VPI (i.e., palatal obturator, palatal lift)

Assessment-History

Medical:

Pregnancy Birth Newborn period Other conditions: heart congenital anomalies Significant illnesses/diseases Audiological

Assessment-History

Speech Therapy:

Enrollment: previous/ current length of enrollment # of sessions per week length per session group/ individual/combination Goals/Progress Treating SLPs name Results of Previous Evaluations

Assessment-History

Parents’ Concerns/Perspective:

Start with a general question: “How do you feel (name) is doing with communication/speech?” Follow-up with specific questions regarding: understandability, articulation skills, hypernasality/NAE, voice, language skills

Assessment-History

School History:

Name of School Grade Enrolled Regular Education/Special Education (or combination) Therapies Enrolled in Special Classes/Educational Help Receive Any teacher concerns regarding learning Results of recent reports/grades

Assessment-History

Psychological Issues:

-Obtain results of any psychological, educational &/or IQ testing, if available.

Assessment-History

Feeding/Swallowing:

Inquire as to any history of difficulty with: sucking, chewing, swallowing -This includes both liquids & solids.

- Any history of nasal regurgitation of liquids -Any issues with textures, temperatures, spiciness/blandness - Swallow studies/Oral Pharyngeal Motility (OPM) studies - History should be from birth to current age

Assessment-History

Peer Interactions:

- First find out if the child has opportunities for peer interactions -Then find out if they have age-appropriate interactions with their peers or if they have difficulties

Determining Nasal Patency

• Need to determine patency (airflow) of each nostril • Need to determine patency for both breathing & production of nasal sounds • If airflow is restricted or obstructed, it may mask

SEVERITY &/OR INCIDENCE

of resonance/NAEs

Determining Nasal Patency cont’d.

Procedure:

1. Tell the patient to blow their nose.

2. Place the mirror under both nostrils (or one at a time).

3. Tell the patient to close their mouth & breath out of their nose.

4. Keep the mirror under the nostrils.

5. Tell the patient to say /m/.

Determining Nasal Patency cont’d.

• Place the mirror under both nostrils (or 1 at a time)

Determining Nasal Patency cont’d.

• Tell the patient to close their mouth and breathe out of their nose.

Determining Nasal Patency cont’d.

• Keep the mirror under the nostrils & tell the patient to say /m/.

Determining Nasal Patency cont’d.

• Variability in Responses

Determining Nasal Patency cont’d.

• Recording responses/information

Recording Nasal Patency Information Nasal Obstruction: Right Nostril Occluded Left Nostril Occluded

a.

Inhalation/exhalation none partial complete none partial complete b.

Sustained /m/ (3 secs.) none partial complete none partial complete (Circle response)

Assessment-Articulation

Intent of Articulation Assessment:

1. To obtain as much information as possible regarding articulation abilities.

Assessment Articulation cont’d.

Intent of Articulation Assessment cont’d.:

2. Use information not only to diagnose articulation/phonological deficit/disorder BUT: a. Determine possible causes for deficit/ disorder b. Determine if attempt to use &/or use enough high pressure consonants to determine VP adequacy c. Determine if compensatory articulations are being used d. Help determine prognosis for improvement with/without speech therapy

Assessment Articulation cont’d.

General Guidelines:

It is very important to

watch the face/nose/mouth!

Allows you to observe: nasal grimace, incorrect placement, facial/neck tension etc.

True for both assessment & therapy.

Assessment Articulation cont’d.

General Guidelines cont’d.:

Watch for

lip & tongue mobility

&/or

restrictions

.

Watch for

dental abnormalities

which might impact correct sound production. This includes

dental appliances

.

Watch for

respiratory abnormalities

.

Assessment Articulation cont’d.

Guidelines:

1. Transcribe the entire production phonetically including correct productions.

2. Note if response was spontaneous or imitative.

Assessment Articulation cont’d.

Guidelines cont’d.:

3. Use “narrow phonetic transcriptions” for errors not transcribable with normal phonetic symbols.

Other Narrow Transcriptions

• Nasal Air Emission / / • Denasal / / • Nasalized Resonance[ ] • Unaspirated [ ] • Unreleased [ ] • Interdental [ ] • Lateralized [ ]

Other Narrow Transcriptions

Transcription Symbols for Compensatory Articulation Errors

Assessment Articulation cont’d.

Guidelines cont’d.:

4. Note any vowel errors.

5. If more than just a few nasal air emissions (NAE) occur, count as errors when scoring.

Assessment Articulation cont’d.

Guidelines cont’d.:

6. Do stimulability testing.

7. Note any differences during conversational speech.

8. Rate the overall intelligibility/understandability of speech.

Assessment Articulation cont’d.

Guidelines cont’d.:

9. Note any

weak pressure consonants

&/or

reduced intra-oral air pressure

.

Assessment Articulation cont’d.

Test Selection:

Consider age of patient, language abilities etc.

Want a test that will

keep the patient’s interest

.

Want to assess sounds in as many positions as possible.

Want to assess as many consonant blends as possible.

Compensatory Misarticulations

• Learned articulation errors • Are mostly errors of PLACEMENT • Are typical to those with “cleft palate speech” • Develop as a means or strategy to overcome structural difficulties due to the cleft • Are used to attempt to obtain valving for high pressure consonants • Become part of child’s phonology • Can be very persistent

Types of Compensatory Misarticulations

• Glottal Stops • Laryngeal Stops • Pharyngeal Stops • Mid-dorsum Palatal Stops • Laryngeal Fricatives • Pharyngeal Fricatives • Velar Fricatives • Mid-dorsum Palatal Fricatives • Posterior Nasal Fricatives • Laryngeal Affricates • Pharyngeal Affricates • Mid-dorsum Palatal Affricates • Posterior Nasal Affricates

Types of Compensatory Misarticulations cont’d.

• Atypical Backing of /l/ • Atypical Backing of /n/ • Atypical Backing of /r/ • Novel or idiosyncratic misarticulations

Glottal Stop / /

• Most common error • Normal sound in many languages – English: vowel initiation • Voiced Stop consonant with glottal placement • Laryngeal / Vocal cord valving – Adduct – Pressure build-up below glottis

GLOTTAL STOP / / • Greater pressure builds up

– Consonant substitution > vowel initiation

• Excessive tension

– Lower vocal tract – > intense opening / closing vocal cords – Ventricular vocal cords adduct / contact

Glottal Stop / /

• Substituted: whole class of stops • Frequently co-articulated – One manner of production – Two places of production • Deviant / nonphonemic place effects manner • Perceptually distinct – Pharyngeal stop / omission

Glottal Stop / /

Laryngeal Stop • Substitution for stop sounds • Base of tongue

– Moves posteriorly toward PPW (posterior pharyngeal wall) – Epiglottis contacts PPW • Momentarily blocking airstream

• Larynx thought to move

– Superiorly – Assist stopping airflow

Pharyngeal Stop

• Lingua-pharyngeal consonant articulation – Contact: tongue base to PPW – Pressure build-up / Sudden release • Manner of production: Stop/Plosive • Contact: high or low • Substitution for /k/ , /g/ • Not used as co-articulation • Voiced / / or unvoiced / /

Pharyngeal Stop

Mid-Dorsum Palatal Stop

• Stop consonant made in approximate place of “y” • Mid-section of tongue (dorsum) contacts mid-section of palate • Typically substituted for /t/ or /k/ (voiceless) & /d/ or /g/ (voiced) • Perceptually is a cross between /t-k/ or /d-g/ • May represent a place compromise between anterior & posterior • May have been learned to use tongue to occlude palatal fistula • Only mid-dorsum compensatory articulations are not behind the uvula for place of articulation • Voiced / / or unvoiced / /

Laryngeal Fricative

• Substitution for fricative sounds • Tongue base – Posterior – Pushes epiglottis toward PPW – Narrows airstream • Constriction – Epiglottis & PPW • Larynx moves up • Variant – Pharyngeal fricative

Pharyngeal Fricative

• Lingua-pharyngeal fricative articulation • Tongue moves posteriorly toward PPW • Dorsum of tongue flattened • Constriction of airstream = frication • Substituted: fricatives & affricates • Co-articulation • Voiced / / or unvoiced / /

Pharyngeal Fricative

Velar Fricative

• Fricative production made at back velar for place of articulation • Similar to /k/ or /g/ but tongue isn’t touching the palate • Common substitution for sibilant fricatives or as distortion of /k/ or /g/ which then lack stop quality due to VP port leak • Seen with dysarthria due to reduced range of movement in back of tongue • Voiced / / or unvoiced / /

Mid-Dorsum Palatal Fricative

• Substitution for fricative sounds • Same positioning as mid-dorsum palatal stop but positioning creates frication • May be place compromise to attempt to achieve valving for airflow • Voiced / / or unvoiced / /

Posterior Nasal Fricative

• May be called velopharyngeal fricative • Turbulent VP fricative articulation occurring with small VP opening • Tongue moves back to help occlude the port (lingual assist), velum approximates PPW but does not touch. Result is constricted airflow through the VP port; velum “flutters” against PPW or adenoid pad • Perceived as frication/”snorting” • May occur as selective substitution for sibilant fricatives & affricates • Can be co-produced with any high pressure consonants • May be obligatory due to VPI/S or learned • Notable occurrence in individuals without clefts as phone specific nasal emission • Symbol: / /

Laryngeal Affricate

• Substitution: affricate sounds Tongue base posterior

– Epiglottis • Brief contact PPW • Then constrict airstream – Stopping – Then frication

• Larynx moves superiorly

Pharyngeal Affricate

• Combines pharyngeal fricative & glottal stop • Less frequent in occurrence than glottal & pharyngeal stops as well as pharyngeal fricatives • Mostly substituted for oral affricates “ch” & “j” • Dorsum of tongue moves posteriorly to contact PPW • Tongue contact constricts airstream to create stopping followed by frication • Does not occur as co-articulation • Voiced / / or unvoiced / /

Mid-Dorsum Palatal Affricate

• Substitution for affricate sounds • Same positioning for mid-dorsum palatal stop but positioning creates affrication • May be place compromise to achieve valving for airflow • Voiced / / or unvoiced / /

Posterior Nasal Affricate

• Substitution for affricate sounds • Posterior dorsum of tongue & velum – Create at VP valve • Stopping • Frication • • Audible NAE / Posterior Nasal Fricative

Amenable to speech treatment

– Tongue placement / Oral airflow

Atypical Backing of /l/

• Backed oral production of /l/ • Move place of production back to velar area • Characteristic of cleft palate speech • Less impact on intelligibility than other compensatory misarticulations • Symbol: / /

Atypical Backing of /n/

• Backed production of /n/ • Placement may be anywhere on palate including velum • Characteristic of cleft palate speech • Less impact on intelligibility than other compensatory misarticulations • Symbol: / /

Atypical Backing of /r/

• Backed oral production of /r/ • Placement is farther back, may be on velum • Characteristic of cleft palate speech • Less impact on intelligibility than other compensatory misarticulations • Symbol: / /

Novel or Idiosyncratic Misarticulations

• Individuals will make their own unique misarticulations • Idiosyncratic misarticulations tend to occur more in patients with cleft palate • Novel/idiosyncratic misarticulations may include compensatory error co-articulated with normal placement production with manner error or placement may be also in error

Observations Regarding Compensatory Misarticulations

• Are active errors • Can be changed in therapy • Need to eliminate/reduce as many as possible prior to FFVN for valid study • Are “stubborn”; therefore, really need to apply the “new pathways” techniques/principles

Assessment-Resonance

• Resonance -hypernasality -assimilative hypernasality -hyponasality -cul-de-sac -denasality -mixed resonance

Assessment Resonance cont’d.

Definitions

• Resonance: -vibratory response of a body or air-filled cavity to frequency of sound -quality of voice resulting from sound vibrations in pharyngeal, oral &/or nasal areas -refers to both perceptual & physical aspects

Assessment Resonance cont’d.

Definitions

• Hypernasality: -excess nasal resonance on vowels & vocalic consonants (i.e., “ir” as in “bird”), glides (“w, y”) or liquids (“l, r”) -transcribed as: ~

Assessment Resonance cont’d.

Definitions

• Assimilative Hypernasality: -excess nasal resonance on vowels in presence of nasal consonants (“m, n, ng”) -transcribed as: ~

Assessment Resonance cont’d.

Definitions

• Hyponasality: -reduction in nasal resonance -affects nasal consonants -is NOT opposite of hypernasality/can co-occur

Assessment Resonance cont’d.

Definitions

• Cul-de-sac Resonance: -blind pouch/passage with only one outlet -resonance sounds as if in a cave -created by trapping resonance (or sound) in back of mouth -tongue placed back in mouth toward pharyngeal wall

Assessment Resonance cont’d.

Definitions

• Denasality: -nasal air flow is completely blocked -prevents nasal air flow for nasal consonants -/m/ sounds like /b/ -/n/ sounds like /d/ ”ng” (as in “ring”) sounds like /g/

Assessment Resonance cont’d.

Definitions

• Mixed Resonance: -combination of hypernasality, assimilative hypernasality, hyponasality, &/or cul-de-sac resonance -can have any combination -severity may vary between resonance types

Assessment Resonance cont’d.

Procedure

Rating Scale:

Numerous rating scales exist Ratings are usually descriptive & numerical Rating is SUBJECTIVE CMHC currently uses a

7-point scale

CPCF Journal (January 2008) article shows how to convert various scales to a 4-point scale

Assessment Resonance cont’d.

Procedure

Rating Scale cont’d.:

CMHC 7-point rating scale: 7 6 5 4 3 2 1 None Slight Mild Mild-Mod Mod Mod-Sev Severe

Assessment Resonance cont’d.

Procedure

Hypernasality:

Areas to Assess: Spontaneous Speech Sample Sustained Vowel Sentence Imitation task

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

Areas to Assess: Spontaneous Speech Sample

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

Areas to Assess: Sustained Vowel /i/

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

1. Place glove on your hand. 2. Tell child you’re putting the glove on because

“in a little while I’m going to gently touch your nose”

.

3. Tell child

“we’re going to practice how long we can say a sound”

.

4. Tell child

“right now my hand with the glove is going to stay over here by me”

.

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

4. Tell child

“I want you to say /i/ for as long as you can”

.

5. Tell child

“Let’s do it together”

.

6. Tell child

“Good! Now this time I want you to say /i/ until my finger is on your side of the table”

.

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

7. Tell child

“Now I want you to say /i/ again for as long as you can (until my finger is on your side of the table). While you say /i/, I’m going to gently open & close your nose”

.

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

Areas to assess: Sentence Imitation Task

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

1. Tell child:

“I want you to say what I say”

.

2.

Say “I see a big black dog”.

3.

“Say it again”. “Good”

4. Do the same with the other 2 sentences:

“Put your feet by the seat.” “He has a beet to eat.”

Assessment Resonance cont’d.

Procedure

Hypernasality cont’d.:

Sentence Imitation Task cont’d.

Assessment Resonance cont’d.

Procedure

Assimilative Hypernasality:

Area to assess: Sentence Imitation Task

Assessment Resonance cont’d.

Procedure

Assimilative Hypernasality cont’d.:

Area to Assess: Sentence Imitation Task cont’d.

Assessment Resonance cont’d.

Procedure

Assimilative Hypernasality cont’d.:

1. Tell child:

“I want you to say what I say”

.

2.

Say “Hand the mean dog some meat”.

3.

Say “The swing is neat and clean”.

Assessment Resonance cont’d.

Procedure

Hyponasality:

Areas to Assess: Sustained nasal /m/ Sentence Imitation Task

Assessment Resonance cont’d.

Procedure

Hyponasality cont’d.:

1. Tell child:

“I want you to say what I say”.

2.

Say “My mama makes lemon jam”.

3.

Say “Nancy is a nurse”.

Assessment Resonance cont’d.

Procedure

Other Resonance Types:

Cul-de-sac, denasality, mixed resonance Specific stimuli not used Rate/make observations regarding while assessing other resonance areas & articulation as well as during conversational speech

Assessment Resonance cont’d.

Procedure

Infant-Toddler Assessment:

1. SLP rates

severity of overall hypernasality

in

spontaneous speech

.

2. SLP rates

severity of overall hyponasality

in

spontaneous speech

.

3. SLP asks

parents to rate severity of hypernasality

.

4. SLP asks

parents to rate severity of hyponasality

.

5. SLP asks if

parents perceive any CHANGES in resonance

. If so,

when & how?

Assessment-Nasal Air Emissions (NAE)

• Nasal air emissions (NAE): -audible -inaudible -nasal grimace -nasal turbulence/rustle

Assessment NAE cont’d.

• Audible Nasal Air Emissions: -oral consonants produced (emitted) through the nose -airstream is heard from the nose -transcribed as: ~

Assessment NAE cont’d.

• Inaudible Nasal Air Emissions: -oral consonants produced through the nose -not heard perceptually -detected by mirror exam

Assessment NAE cont’d.

• Nasal Grimace: (NG) -noticeable movement of nose during speech -movement may occur at nares, mid-nose, nasal bridge -movement may be unilateral or bilateral -movement occurs in attempt to achieve velopharyngeal closure -movement is subconsciously used to move oral sound back to oral cavity from nasal cavity

Assessment NAE cont’d.

• Nasal Turbulence/Rustle: (NT) -oral consonant sound occurs during partially opened velopharyngeal valve -air flow is turbulent with noted noise/rustle

Assessment NAE cont’d.

Procedure

Nasal Air Emissions-Audible & Inaudible:

Areas to Assess: Isolation CV Syllables Phoneme-Loaded Sentences Stop/Plosive Fricative/Affricate Mixed Nasal/Oral Loaded Words & Sentence(s) Conversational Speech Single High Pressure Consonant Words (IPAT) Stimulability for Correction

Assessment NAE cont’d.

Procedure

• Area to Assess: Isolation

Assessment NAE cont’d.

Procedure

Isolation:

1. Tell child

“we’re going to say some sounds”

.

2.

“First we will do them without my mirror.”

3.

“Then we will do them with my mirror.”

4.

“Say /s/”.

Assessment NAE cont’d.

Procedure

Isolation cont’d.:

5.

“Say /p/”.

6.

“Say /t/”.

7.

“Say /k/”.

8.

“Say “sh”.

Assessment NAE cont’d.

Procedure

Isolation cont’d.:

9.

“Now let’s do them again with my mirror”.

10. Repeat each sound while holding the mirror under the nostril(s).

Assessment NAE cont’d.

Procedure

• Area to Assess: CV Syllables

Assessment NAE cont’d.

Procedure

CV Syllables:

1. Tell child

“we’re going to say some more sounds”.

2.

“First we will do them without my mirror.”

3.

“Then we will do them with my mirror.”

4.

“Say /sa/”.

Assessment NAE cont’d.

Procedure

CV Syllables cont’d.:

5.

“Say /pa/”.

6.

“Say /ta/”.

7.

“Say /ka/”.

8.

“Say “sha”.

Assessment NAE cont’d.

Procedure

CV Syllables cont’d.:

9.

“Now let’s do them again with my mirror”.

10. Repeat each sound while holding the mirror under the nostril(s).

Assessment NAE cont’d.

Procedure

• Areas to Assess: Phoneme-Loaded Sentences

Assessment NAE cont’d.

Procedure

Phoneme-Loaded Sentences:

1. Tell child

“now we’re going to say some sentences”.

2.

“First we will do them without my mirror.”

3.

“Then we will do them with my mirror.”

4.

“Say ‘Peter has a paper puppy”.

Assessment NAE cont’d.

Procedure

Phoneme Loaded Sentences cont’d.:

5.

“Say ‘Buy a baby bib’.”

6.

“Say ‘Tell teddy to try’.”

7.

“Say ‘Daddy did the dishes’.”

8.

“Say ‘Katie likes cookies’.”

9.

“Say ‘Go get a bigger egg’.”

Assessment NAE cont’d.

Procedure

Phoneme Loaded Sentences cont’d.:

10.

“Now let’s do them again with my mirror”.

11. Repeat each of the plosive-loaded sentences while holding the mirror under the nostril(s).

Assessment NAE cont’d.

Procedure

Phoneme Loaded Sentences cont’d.:

12.

“Now we have some more sentences to do”.

13.

“Say ‘Silly Sue eats icicles’.”

14.

“Say ‘Zippers are easy to close’.”

15.

“Say ‘Should I wash the dishes?’.”

16.

“Say ‘The garage hid the treasure’.”

Assessment NAE cont’d.

Procedure

Phoneme Loaded Sentences cont’d.:

17.

“Say ‘Chad’s teacher was at church’.”

18.

“Say ‘Jack wore a soldier’s badge’.”

19.

“Say ‘Feed five frogs fish food’.”

20.

“Say ‘Vic veered everywhere’.”

21.

“Say ‘Thank you for the birthday present’.”

Assessment NAE cont’d.

Procedure

Phoneme Loaded Sentences cont’d.:

22.

“Now let’s do them again with my mirror”.

23. Repeat each fricative & affricate-loaded sentence while holding the mirror under the nostril(s).

Assessment NAE cont’d.

Procedure

• Area to Assess: Mixed Nasal/Oral Loaded Words & Sentence(s)

Assessment NAE cont’d.

Procedure

Mixed Nasal/Oral Loaded Words & Sentence(s):

1. Tell child

“say ‘hamper hamper hamper’.”

2.

“Good! Now do it again as fast & as many times as you can.”

3.

“Now say ‘donna donna donna’.”

4.

“Good! Now do it again as fast & as many times as you can.”

Assessment NAE cont’d.

Procedure

• Area to Assess: Conversational Speech

Assessment NAE cont’d.

Procedure

Conversational Speech:

Areas to Rate/Observe in regard to NAEs: Present vs. Absent Pervasive vs. Inconsistent vs. Occasional Nasal Turbulence Nasal Grimacing

Assessment NAE cont’d.

Procedure

• Area to Assess: Single High Pressure Consonant Words

Assessment NAE cont’d.

Procedure

• Area to Assess: Single High Pressure Consonant Words cont’d.

Stimuli:

Iowa Pressure Articulation Test (IPAT)

Assessment NAE cont’d.

Procedure

Iowa Pressure Articulation Test (IPAT):

Single Items Two-Item Blends /-k-/ MONKEY _____ / sm/ POSSUM _____ “-ker” CRACKER _____ /-g-/ WAGON _____ / ks/ BOOKS _____ “-ork” FORK _____ /k / CAT _____ “-per” PAPER _____ “-sher” WASHER _____ /g-/ GIRL _____ /sk-/ SKY _____ /gr-/ GRASS _____ /t-/ TABLE _____ /sm / SMOKE _____ “-ger” TIGER _____ /-f-/ TELEPHONE _____ /sn-/ SNAKE _____ /-lf/ WOLF _____ /-f/ LEAF _____ /st-/ STOVE _____ /-z-/ SCISSORS _____ /kr-/ CRAYON _____

3-Item Blends

/-s-/ PENCIL _____ /sp-/ SPOON _____ /s-/ SOAP _____ /tr-/ TREE _____ /-mps/ STAMPS _____ “sh-” SHOE _____ /kl-/ CLOWN _____ /str-/ STRING _____ /-s/ BUS _____ /gl-/ GLASS _____ /-g/ PIG _____ /bl-/ BLOCKS _____ “-sh” FISH _____ /br-/ BROOM _____ “j-” JEEP _____ /dr-/ DRUM _____ /-k/ BOOK _____ /tw-/ TWELVE _____ “-sh-” DISHES _____ /pl-/ PLATE _____

Assessment NAE cont’d.

Procedure

IPAT cont’d.:

1. Tell child

“we’re going to same some words without pictures”.

2.

“I want you to say what I say.”

3.

“Say ‘monkey’ , say ‘wagon’ etc.

Assessment NAE cont’d.

Procedure

• Area to Assess: Stimulability for Correction

Assessment NAE cont’d.

Procedure

Overall Rating of Nasal Air Emissions:

Present vs. Absent Audible Inaudible Pervasive/Inconsistent/Occasional Nasal Turbulence Nasal Grimace (describe) Severity Rating: none/slight/mild/mild-moderate/moderate/moderate-severe/ severe

Assessment NAE cont’d.

Procedure

Infant-Toddler Assessment:

1. SLP performs

overall rating of nasal air emissions

.

2. Note if

stimulable for correction

.

3. Note if

could not test (CNT)

or

did not test (DNT)

.

Assessment-Velopharyngeal Adequacy (VPA) Procedure

• Intent: To

PERCEPTUALLY

determine VP adequacy

Assessment-Velopharyngeal Adequacy (VPA) cont’d.

Procedure

VP Ratings:

Velopharyngeally Adequate (VP/A) or Velopharyngeally Inadequate (VPI/A)

Assessment-Velopharyngeal Adequacy (VPA) cont’d.

Procedure VP Ratings cont’d:

Other possibilities: Borderline VPI/A Questionable

Assessment-Velopharyngeal Adequacy (VPA) cont’d.

Procedure VP Ratings cont’d.:

Other Possibilities cont’d.: Unable to determine at this time Could not test

Assessment-Language Procedure

• Intent: to determine if language skills are age-appropriate

Assessment Language cont’d.

Procedure

Guidelines for Test Selection:

1. Assess receptive & expressive skills 2. Choose an age/developmentally-appropriate test 3. With most patients, want in-depth testing (vs. screening)

Assessment Language cont’d.

Procedure

Additional Information:

If there are

time

or

cooperation restraints:

At

CMHC

we

prioritize EXPRESSIVE over receptive

due to the

greater depth of information gained OR

We

DEFER language testing

to the

treating SLP

Assessment-Voice Procedure

• Intent: to assess voice for abnormalities in pitch, volume, &/or quality

Assessment Voice cont’d.

Procedure

Assessment of Pitch:

Make observations regarding

pitch level-high, low, normal

Note if

vocal fry

is present due to talking at bottom of pitch range.

Note if

vocal strain

is heard due to talking at top of pitch range.

Note if able to

vary pitch

or is the

pitch range limited/monotonous.

Observe if using

diplophonia

(talking with 2 simultaneous pitch levels).

If time permits, attempt to

modify level/range etc

.

BE CAREFUL NOT TO CONFUSE HIGH PITCH WITH HYPERNASALITY!!!

They may

CO-OCCUR,

but are

not synonymous

.

Assessment Voice cont’d.

Procedure

Assessment of Volume:

Note if volume is

too soft/quiet, excessively loud, cannot be maintained over time

(varies).

FREQUENTLY low pressure

(due to VP valve issues)

reduces the volume &/or ability to maintain a consistent volume

.

If time permits, attempt to

modify volume

.

Assessment Voice cont’d.

Procedure

Assessment of Quality:

Note if: hoarseness breathiness huskiness raspiness harshness aphonic

Assessment-Fluency Procedure

• Intent: to assess if speech is fluent or dysfluent

Assessment-Oral Mechanism/Oral Peripheral Examination Procedure

• Intent: to assess oral mechanism for structure & function deficits

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Selection of Protocol: formal or informal

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Positioning of Patient: eye level at level of oral cavity seated, erect

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Initial Observations: Note if cleft exists & type (none, overt, submucous)

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Initial Observations:

Overt Cleft

• Note if lip &/or palate • Note if unilateral (if so, note if right or left) or bilateral or midline or facial • Note if complete or incomplete • Note if repaired or unrepaired

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Initial Observations:

Submucous Cleft Palate

• Note if bifid uvula • Note if notch in hard palate • Note if muscular diastasis • Note if repaired or unrepaired • Note if occult

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed: Lips Tongue Nose Teeth Mandible/Maxilla Alveolus Hard Palate Soft Palate Other

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed: Lip Movements Tongue Movements Soft Palate Movement

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Lips

• Assess/Observe: Symmetry scarring thinness/thickness continuity of muscle notching limited mobility/tight frenulum protruding premaxilla open resting posture lip pits

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed:

Lips

• Assess/Observe: protrusion retraction approximation

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Tongue

• Assess/Observe: size shape scarring lingual frenulum

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed:

Tongue

• Assess/Observe: protrusion depression lateralization elevation-outside oral cavity elevation-inside oral cavity circling lips clicking

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Nose

• Assess/Observe: size/width shape nostrils (opening & nasal alae) tip nasal bridge columella septum scarring symmetry

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed:

Nose

• Assess/Observe: patency obstruction

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Teeth

• Assess/Observe: occlusal relationship incisor relationship supernumerary teeth rotated teeth missing teeth crowding primary/permanent condition (cavities) appliances

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed:

Teeth

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• How to Assess Teeth:

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Mandible/Maxilla

• Assess/Observe: micrognathia macrognathia protrusion retrusion arch formation/collapse hypoplasticity mid-face retrusion

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Alveolus

• Assess/Observe: residual cleft fistula

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structured Assessed:

Hard Palate

• Assess/Observe: repaired vs. unrepaired width shape/height of palatal vault scarring/fissures/protuberance surgical alterations fistula palpated notch coloring

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Soft Palate

• Assess/Observe: repaired vs. unrepaired bifid uvula zona pellucida length/width/thickness shape during phonation symmetry at rest & during phonation scarring/surgical alterations fistula

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Functions Assessed:

Soft Palate

• Assess/Observe: degree of movement direction of movement fluidity of movement pharyngeal movement

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Other

• Assess/Observe: tonsils pharynx epiglottis craniofacial/other anomalies (eyes, ears, hands, etc.)

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Structures Assessed:

Other cont’d.

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Additional Assessment/Technique Information: • Compare

normal vs. abnormal

• Judgment improves with

experience

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Additional Assessment Technique/Information: • Assessing

infants & toddlers

Assessment-Oral Mechanism/Oral Peripheral Examination cont’d.

Procedure

• Additional Assessment Technique/Information: • Assessing the

less cooperative patient

Assessment-Order of Rationale

Order of Assessment:

1. History 2. Nasal Patency 3. Articulation 4. Iowa Pressure Articulation Test 5. Nasal Air Emissions-isolation, syllable, sentences, mixed words/sentences 6. Hyponasality 7. Assimilative Hypernasality 8. Hypernasality-sustained vowel, sentence imitation (9. Language) 10. Oral mechanism examination

Assessment-Order of Rationale cont’d.

John Wesley saying: Do all the good you can By all the means you can In all the ways you can In all the places you can To all the people you can As long as ever you can

Assessment-Order of Rationale cont’d.

Order of Assessment cont’d.:

1. History: I have reviewed medical chart/reports etc. prior to seeing the patient, but I can

ask caregivers questions

while child

plays with an age-appropriate toy

(NOTE: gives me time to

observe child

).

2. Nasal Patency: need to establish as impacts articulation/resonance/NAE/VP adequacy test results 3. Articulation: If

ALL

I get done is this, I can at least make some observations regarding resonance,NAE, VP adequacy, voice, expressive vocabulary, ability to follow directions etc.

Assessment-Order of Rationale cont’d.

Order of Assessment cont’d.:

4. Iowa Pressure Articulation Test: rather

non-invasive

test measure & can make additional observations similar to those on articulation test 5. Nasal Air Emissions: testing

without the mirror

is

non-invasive/non-threatening

-testing

with the mirror MAY BE threatening

to some patients 6/7/8. Hyponasality/Assimilative Hyponasality/Hypernasality: The first 2 are also

non invasive/non-threatening HOWEVER

testing for

HYPERNASALITY

involves use of

GLOVES

. This can be

stressful/threatening

for many children. If I were to

START

with tests involving

GLOVES

, I may lose the child entirely and, therefore,

accomplish little testing

& get

minimal diagnostic information

.

Assessment-Order of Rationale cont’d.

Order of Assessment cont’d.:

9. Language: As covered previously, this is a lower priority than the other areas.

10. Oral Mechanism Examination: This is another area that may be

stressful/threatening

to the children. REMEMBER for most young children, people look in their mouths when they

aren’t feeling well

(i.e., strep test).

ALSO, although each

discipline

on the

team

looks in the child’s mouth for a different purpose (i.e., dental vs. plastics vs. speech vs. ENT), usually

at least one

is able to accomplish this. In other words, if I

CAN’T/DON’T

get this information someone should have some of it. OF COURSE, if you are the

only person doing the assessment (not part of a team)

, this may be of a little more importance.

I always try to keep the

impact GRAND SCHEME

in mind. If I

DON’T

get this done, how

negatively will it

my diagnostics/ability to help the child? Am I

better off DIFFERING till another time so as to not alienate the patient OR is it imperative that I accomplish this on this date?

Other Issues Impacting Cleft Lip/Palate &/or Velopharyngeal Inadequacy

• Possible Issues: feeding problems development/cognition educational issues psychosocial issues hearing problems multiple anomalies syndromes genetic issues

Importance of the Team Approach to Treatment

Why team management?

Benefit for the patient/family Benefit for the professionals

Importance of Team Approach to Treatment cont’d.

• The

GREATEST IMPORTANCE

is that

team care

helps to provide the the patient!

BEST OUTCOME

for

Guidelines for Referrals for Perceptual &/or FFVN (Instrumental) Evaluations

• Perceptual • FFVN

Perceptual Guidelines including Articulation

• Perceptual Evaluation performed within 6 months of FFVN • Uses some high pressure consonants • Validity of study • Can be prior to study or same day of • Actually attempting to use the palate • Scheduling variables: behavior, fatigue, time factor (distance traveled)

Necessary Therapy Guidelines

• A good solid course of therapy should be provided prior to consideration for either perceptual or FFVN evaluation.

• At least one individual, 45-minute session per week for a minimum of 4 months, but preferably longer.

• The more high pressure consonants the child has or is attempting, the more valid the study, the more likelihood we will be able to truly help them.

Age Guidelines

• Majority are at least 4 years of age or older • Cooperation • High pressure consonants • Age normally distinguish oral vs. nasal sounds (2 years old)

FFVN Teams at CMHC

• With Plastic Surgery • 3 speech/language pathologists (SLP) • Claudia Magers, MS, CCC-SLP • Sally Helton, MS, CCC-SLP • Sabrina Wallace, MS, CCC-SLP • With ENT • 1 SLP • Claudia Magers, MS, CCC-SLP

Referral Guidelines for FFVN

• Refer patients: • Suspect velopharyngeal inadequacy (VPI/A) • Suspect nasal obstruction • Who present with disorders of vocal production (pitch, quality, intensity) • Who present with possible or known disorder of structure &/or function of larynx

Referral Guidelines for FFVN Suspect Velopharyngeal Inadequacy

• Cleft Palate • Neurological impairments, especially with oral motor involvement • Pre-tonsillectomy &/or adenoidectomy at high risk for VPI/A following surgery • Post-tonsillectomy &/or adenoidectomy

Referral Guidelines for FFVN Suspect Velopharyngeal Inadequacy cont’d.

• Hypernasal vocal resonance • Speech impairment including compensatory articulations, reduced intra-oral air pressure, &/or nasal air emissions • Pre-maxillary advancement at risk for VPI/A following advancement

Referral Guidelines for FFVN Suspect Nasal Obstruction

• Hyponasal or denasal vocal resonance • Post-pharyngeal flap surgery • Pre-tonsillectomy &/or adenoidectomy • Obstructive Sleep Apnea

Referral Guidelines for FFVN Present with Vocal Disorders

• Affecting: • Pitch • Quality • Intensity

Referral Guidelines for FFVN Present with Laryngeal Disorder

• Possible or known disorder of structure &/or function of larynx • i.e., vocal cord nodules, polyps • i.e., vocal cord dysfunction

Guidelines Impact on Success of Studies

• Allow to be highly successful in completion of valid studies • Don’t do unnecessary studies • “Don’t burn bridges” • Applies to both perceptual & age guidelines

Guidelines for Referral for Perceptual &/or FFVN (Instrumental) Evaluation

• If in doubt, give us a call!

• At 816-234-3677 ask to speak to Claudia Magers, MS, CCC-SLP (Toll Free: 1-888-239 8152) • At 913-696-5750 ask to speak to either Sally Helton, MS, CCC-SLP or Sabrina Wallace, MS, CCC-SLP (Toll Free: 1-888-460-6432)

Guidelines for Referral to Children’s Mercy Hospitals & Clinics Cleft Palate/Craniofacial Teams

• # of Teams/Plastics Surgeons: 3 Virender K Singhal, MD, MBA Shao Jiang, MD Alison Kaye, MD Location of Services: Children’s Mercy Hospital, 24 th & Gillham Rd., Kansas City, Missouri Children’s Mercy South/College Blvd. Clinics 5808 W. 110 th St./5520 College Blvd.

Overland Park, Kansas Contact Person for Scheduling: Stephanie Taylor, Cleft Palate Coordinator 816-234-3677 (Hearing & Speech @ CMHC @ Gillham Rd.) Toll Free: 888-239-8152

Final Thoughts

• Partnership: -CMHC SLPs are in partnership with you the treating SLP -we all ultimately want the best outcome possible for these children

Contact Information

• Sally Helton Hearing & Speech 913-696-5756 (direct line) [email protected]

Initial contact: by phone Authorization/Releases

“The Bottom Line”

• I view these children as jigsaw puzzles. They come with the all the pieces and it is my job to figure out how they fit together.

Closing

Good luck with your diagnostics & therapy for your patients/students with cleft lip & palate &/or VPI!